Spinal Exostosis in a Boy with Multiple Hereditary Exostoses

Abstract

We report on a 13-year-old boy who presented with multiple hereditary exostosis and had development of back pain, associated with neurological deficits, and was found to have exostoses in the spinal canal. Spine radiograph showed a cauliflower-like abnormality of multiple exostoses of the posterior arch (pedicle) of the thoracic vertebrae (T3–5). Reformatted CT scanning revealed the simultaneous development of intra- and extraspinal osteochondromatosis of T3–5. The spinal cord was compressed by the intraspinal exostosis. Our patient was surgically treated for intraspinal exostoses and showed cessation of neurological deficits. We report what might be a rare association of spinal cord compression in a patient with multiple hereditary exostoses.

Osteochondroma of Lower Dorsal Spine in Hereditary Multiple Exostosis Causing Spinal Cord Compression: Report of a Case and Review of the Literature

“…Although aetiologically not clear, OCs are originated from the separation of epiphyseal growth plate cells followed by herniation through the periosteum adjacent the growth plate. 26 The vertebral OC are more common in younger male patients as seen in our case. 22 About 1% and 4%…”

The Reasons for Back Pain in Children

“…It is often asymptomatic but when developing within the neural arch may cause neurological symptoms. Surgical treatment is advised in these cases (Figure 11) [17].…”