Spectrum of MRI Appearance of Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome in Primary Amenorrhea Patients

Boruah, Deb Kumar; Sanyal, Shantiranjan; Gogoi, Bidyut B.; Mahanta, Kangkana; Prakash, Arjun; Augustine, Ann Mary; Achar, Sashidhar; Baishya, Hiranya

doi:10.7860/jcdr/2017/29016.10317

Cited by 28 publications

(38 citation statements)

References 26 publications

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“…5 In the past decade, a number of studies have studied rudimentary Mullerian remnants in MRKH patients. [5][6][7][8][9][10][11] Presence of rudimentary uterine buds was documented by both the readers with good interobserver agreement. Uterine buds were mostly bilateral.…”

Section: Discussionmentioning

confidence: 95%

“…18,19 Reporting this fact remains important, to prevent torsion, incarceration and ischaemia of these ectopic inguinal ovaries. 10 Excessive mobility of ovaries and weak suspensory ligaments have been hypothesized as possible causes for inguinal location of ovaries. [19][20][21] Renal anomalies are known to be one of the commonly associated non-gynaecologic anomalies in Type II MRKH syndrome.…”

Section: Discussionmentioning

confidence: 99%

“…In the past decade, there has been an increasing interest in the role of MRI in pre-operative assessment of MRKH syndrome. [5][6][7][8][9][10][11] Reproducibility of MRI features in intricate evaluation of anatomy including Mullerian remnants has still not been extensively researched. The purpose of this study was to assess the interobserver reproducibility of pelvic MRI anatomy in MRKH syndrome and substantiate its role as a non-invasive alternative to diagnostic laparoscopy.…”

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confidence: 99%

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MRI evaluation of pelvis in Mayer–Rokitansky–Kuster–Hauser syndrome: interobserver agreement for surgically relevant structures

Bhayana

Ghasi

2019

The British Journal of Radiology

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The paired Mullerian or paramesonephric ducts fuse between 6 and 11 weeks of gestation to form uterus, cervix and upper two-thirds of vagina. Mullerian duct anomalies (MDA) result from disruption in any of the three stages of uterine development, i.e. organogenesis, fusion or septal resorption. 1 Ovaries develop from primordial germ cells, while lower one-third of vagina develops from sinovaginal bulb. Owing to the different embryological origins, ovaries and lower third of vagina are not involved in MDA. 2 The prevalence of MDA is reported to be 1-5%. 2 American Fertility Society (AFS), has classified MDA into seven basic types, from Type I to Type VII. 3 Out of these seven types, Type I MDA also called as Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome, which reportedly accounts for nearly 15% of total case load. 2 MRKH syndrome is characterized by complete/partial agenesis of uterus and upper two-thirds of vagina, with normal bilateral ovaries,

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Section: Discussionmentioning

confidence: 95%

Section: Discussionmentioning

confidence: 99%

mentioning

confidence: 99%

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MRI evaluation of pelvis in Mayer–Rokitansky–Kuster–Hauser syndrome: interobserver agreement for surgically relevant structures

Bhayana

Ghasi

2019

The British Journal of Radiology

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“…However, due to technical difficulties, the results can sometimes be inconclusive [6]. MRI is the imaging modality of choice for the confirmation of diagnosis and is also useful in the identification of any associated malformations [7,8]. It is worth mentioning that Preibsch et al have shown an excellent correlation between MRI and laparoscopy findings in patients with MRKH syndrome [9].…”

Section: Discussionmentioning

confidence: 99%

A rare form of Mayer-Rokitansky-Küster-Hauser syndrome: Case report and review of literature

Dandan

Hassan

Alsaihati

et al. 2019

Case Reports in Women's Health

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Introduction Primary amenorrhea is failure to reach menarche. Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is the second most common cause of primary amenorrhea, after gonadal dysgenesis. Herein, we report a rare case of an unusual subtype of MRKH syndrome. Case Report This report describes the case of a 28-year-old woman with primary amenorrhea and coital difficulties. On examination, she had normal secondary sexual characteristics but a blind-ending vagina. Her hormonal profile was within normal limits; ultrasound examination was inconclusive due to technical difficulties. Subsequently, she underwent pelvic magnetic resonance imaging, which revealed bilateral rudimentary uterine horns in the presence of normal ovaries and normal length of a blind-ending narrow vagina. Conclusion MRKH syndrome with bilateral rudimentary uterine horns and normal-length vagina is an unusual form of Müllerian agenesis.

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“…MRI can depict the distance of an obstructed vagina from the perineum and the thickness of a vaginal septum or atretic segment. MRI examination can accurately measure the gap between the neck and rectum of the urethra and provide references for the selection of surgical methods [ 21 ]. However, MRI could confirm the pelvic mass derived from ovaries but could not distinguish between polycystic ovary and multilocular ovarian serous cystadenoma.…”

Section: Differential Diagnosismentioning

confidence: 99%

Diagnosis and Management of Ovarian Tumor in Mayer-Rokitansky-Küster-Hauser (MRKH) Syndrome

Miao

Wen

Huang

et al. 2018

BioMed Research International

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In the most recent publications on Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, the uterine remnants and ovaries in patients may develop uterine remnant leiomyoma, adenomyosis, or ovarian tumor, and this can lead to problems in differential diagnosis. Here we summarize the diagnosis methods and available interventions for ovarian tumor in MRKH syndrome, with emphasis on the relevant clinical findings and illustrative relevant case. According to the clinical findings and illustrative relevant case, with the help of imaging techniques, ovarian tumors can be detected in the pelvis in patients with MRKH syndrome and evaluated in terms of size. Laparoscopy could further differentiate ovarian tumors into different pathological types. In addition, laparoscopic surgery not only is helpful for the diagnosis of MRKH combined ovarian tumor, but also has a good treatment role for excising ovarian tumor at the same time. Moreover, laparoscopic removals of ovarian tumor can be considered as a safe and reliable treatment for conservative management.

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Spectrum of MRI Appearance of Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome in Primary Amenorrhea Patients

Cited by 28 publications

References 26 publications

MRI evaluation of pelvis in Mayer–Rokitansky–Kuster–Hauser syndrome: interobserver agreement for surgically relevant structures

MRI evaluation of pelvis in Mayer–Rokitansky–Kuster–Hauser syndrome: interobserver agreement for surgically relevant structures

A rare form of Mayer-Rokitansky-Küster-Hauser syndrome: Case report and review of literature

Diagnosis and Management of Ovarian Tumor in Mayer-Rokitansky-Küster-Hauser (MRKH) Syndrome

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