Solitary intrahepatic biliary cyst: Diagnostic and therapeutic strategy

Diagnostic challenge of large congenital liver cyst in the newborn

“…2,3 It can be further subdivided as simple liver cyst (SLC), which contains non-bilious fluid and has no connection to the biliary tract, and SIBC or bile lake, which contain bile and have some connection to the biliary tract. 4 SLC accounted for most of the prenatally detected and postnatally diagnosed liver cysts. 5 SLC arise from maldeveloped bile ducts, typically unilocular and usually never accompanied with cysts in other organs.…”

“…3 Asymptomatic SIBC can be observed on periodic USG. 3,4 For symptomatic cysts and cysts with insufficient drainage into the intestine, internal drainage via cystoenterostomy or Roux-en-Y hepaticojejunostomy has been recommended. 3 Choledochal cysts (types I-IV) are congential cystic lesions of extrahepatic bile ducts formed secondary to abnormalities in the pancreaticobiliary junction.…”

Congenital Solitary Intrahepatic Biliary Cyst in a Newborn: Report of a Case

“…1,3 It can be further classifi ed as simple SLC and SIBC. 2 The etiology of SLC is unknown. It has been hypothesized that obstruction of aberrant bile ducts from infection or as a result of a vascular disruption during the fetal period can be a cause.…”

“…They are unilocular, benign lesions of the liver and can be defi ned as a "simple cyst" or a "biliary cyst" according to the composition of the cyst fl uid and the cyst's anatomical relationship with the biliary tree. 1,2 Although SLCs are usually diagnosed as an incidental fi nding in adults, they are often symptomatic in childhood, even in newborns, and they may be detected incidentally by prenatal ultrasonography (USG). 1,3 Ultrasonography or computed tomography (CT) is widely used for the diagnosis of SLCs; however, their differential diagnosis from other intra-abdominal benign and malignant cystic lesions of the newborn may be diffi cult.…”

The diagnostic and therapeutic approach for the congenital solitary liver cysts

“…Parsiyel eksizyon sonrası kolanjit, sepsis, kistin tekrarlaması gibi karmaşaların görülmesi de hepatikojejunostomi, hepatik rezeksiyon gibi girişimleri gerektirir (2,13) . Perkütan drenajda yineleme oranları çok yüksektir ve yalnızca tanısal amaçlı ve yakınmaların acil kontrolü için kullanılmalıdır (3,20) . Perkütan drenaj sonrası alkol ile skleroterapi erişkinlerde bildirilmiştir, ancak ön-cesinde doğru histolojik tanı konmasını gerektirir ve çocuklarda kullanımı sınırlıdır (5,17,21) .…”