Síndrome de Sweet associada a linfoma de Hodgkin: relato de caso

Miranda, Carolina Villela da Rocha; Filgueiras, Fernanda de Marca; Obadia, Daniel Lago; Gripp, Alexandre Carlos; Alves, Maria de Fátima Scotelaro Guimarães

doi:10.1590/s0365-05962011000500025

Cited by 6 publications

(1 citation statement)

References 8 publications

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“…More and more cases have been described to be associated with malignancies, particularly myeloplastic syndrome and, less frequently, other hematologic malignancies or solid tumors [ 5 , 7 ]. Approximately 21% of patients with SS have an underlying malignancy [ 8 ]. Some authors consider association with MDS to be more frequent, while others sustain the link with AML, but the majority of articles agree that these two hematological pathologies represent more than 80% of MASS [ 5 ].…”

Section: Introductionmentioning

confidence: 99%

Sweet Syndrome Associated with Myelodysplastic Syndrome—A Review of a Multidisciplinary Approach

Ferea

Mihai

Bălan

et al. 2023

Life

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Sweet syndrome (SS) is a rare disease described as a febrile neutrophilic dermatosis with acute onset, the pathogenesis of which has not yet been elucidated. The syndrome is characterized by the sudden onset of erythematous infiltrated papules or plaques located on the upper body and is associated with fever, leukocytosis and neutrophilia. The lesions show a dense dermal infiltration with mature neutrophils. The condition is responsive to systemic steroids. The central nervous system, bones, muscles, eyes, ears, mouth, heart, lung, liver, kidneys, intestines, and spleen may be affected by SS as extracutaneous manifestations. More and more cases have been found to be associated with malignancies, particularly myelodysplastic syndrome, and, less frequently, other hematologic malignancies or solid tumors. Approximately 21% of patients with SS have an associated malignancy and up to 80% of MASS cases are associated with hematological diseases, predominantly myelodysplastic syndrome (MDS) or acute myeloid leukemia (AML). Myelodysplastic syndrome is a clonal disease of the bone marrow characterized by inefficient hematopoiesis, dysplasia of the bone marrow and peripheral cytopenias. Affected patients have a high risk of leukemic transformation. After analyzing later studies and current practical aspects regarding MDS-related SS, we suggest an algorithm for evaluating these patients.

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Section: Introductionmentioning

confidence: 99%

Sweet Syndrome Associated with Myelodysplastic Syndrome—A Review of a Multidisciplinary Approach

Ferea

Mihai

Bălan

et al. 2023

Life

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Sweet Syndrome: A Review and Update

Villarreal-Villarreal

Ocampo‐Candiani

Villarreal‐Martínez

2016

Actas Dermo-Sifiliográficas

108

100

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Sweet Syndrome: A Review and Update

Villarreal-Villarreal

Ocampo‐Candiani

Villarreal‐Martínez

2016

Actas Dermo-Sifiliográficas (English Edition)

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Sweet syndrome is the most representative entity of febrile neutrophilic dermatoses. It typically presents in patients with pirexya, neutrophilia, painful tender erytomatous papules, nodules and plaques often distributed asymmetrically. Frequent sites include the face, neck and upper extremities. Affected sites show a characteristical neutrophilic infiltrate in the upper dermis. Its etiology remains elucidated, but it seems that can be mediated by a hypersensitivity reaction in which cytokines, followed by infiltration of neutrophils, may be involved. Systemic corticosteroids are the first-line of treatment in most cases. We present a concise review of the pathogenesis, classification, diagnosis and treatment update of this entity.

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Síndrome de Sweet associada a linfoma de Hodgkin: relato de caso

Cited by 6 publications

References 8 publications

Sweet Syndrome Associated with Myelodysplastic Syndrome—A Review of a Multidisciplinary Approach

Sweet Syndrome Associated with Myelodysplastic Syndrome—A Review of a Multidisciplinary Approach

Sweet Syndrome: A Review and Update

Sweet Syndrome: A Review and Update

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