Segmental hemangiomas of the upper airway

Abstract

A high percentage of patients with V3 cutaneous hemangiomas (29%) will manifest with upper airway involvement, the distribution of which is segmental. Treatment should take this diffuse pattern of involvement into consideration.

Current treatment of parotid hemangiomas

“…Parotid hemangiomas present as a rapidly growing mass in the preauricular area. They may be part of a segmental V3 hemangioma, in which case there is invariably cutaneous involvement and, in 29% of cases, airway involvement,11 or they may be isolated focal hemangiomas. Focal hemangiomas are located only in the parotid region involving the parotid gland.…”

Diagnosis and management of hemangiomas and vascular malformations of the head and neck

“…The segmental distribution of hemangiomas can also be found within the upper aerodigestive tract. In these patients, superficial and flat lesions are present along the mucosal surfaces of the floor of mouth, lip, tongue, pharynx, hypopharynx, and larynx (O et al , 2009). Rarely are the flat lesions symptomatic unless the trachea or subglottis is involved.…”

Airway hemangiomas in PHACE syndrome

“…All subjects underwent direct laryngoscopy and rigid bronchoscopy by a pediatric otolaryngologist and pediatric anesthesiologist. Airway hemangiomas were photo‐documented and classified as focal or segmental 9, 14. Prior studies defined focal airway hemangiomas as limited to the subglottis and segmental airway hemangiomas as located outside of the subglottis 9, 14.…”

“…Airway hemangiomas were photo‐documented and classified as focal or segmental 9, 14. Prior studies defined focal airway hemangiomas as limited to the subglottis and segmental airway hemangiomas as located outside of the subglottis 9, 14. For this study, we further classified subglottic hemangiomas as unilateral, bilateral, or circumferential.…”

“…The presence of segmental facial cutaneous hemangiomas also increases the likelihood of airway hemangioma. A recent study demonstrated that 29% of subjects with segmental cutaneous hemangioma involving skin arising from the mandibular prominences (so‐called S3, also known as beard‐distribution ), had associated airway hemangiomas 9…”