Segmental absence of intestinal musculature: an increasingly reported pathology

Davis, James S.; Ryan, Mark L.; Shields, John; Sola, Juan E.; Pérez, Eduardo A.; Neville, Holly L.; Rodríguez, Maria M.

doi:10.1016/j.jpedsurg.2012.01.002

Cited by 17 publications

(28 citation statements)

References 14 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…It has been stated that affected segments may be nearly normal at visual/gross inspection or may look like a small herniation of the intestinal wall. In such cases, the most obvious consequence is the risk of perforation [1,3]. In some of the literature, some speculate that SAIM may be a common condition that is not recognized.…”

Section: Discussionmentioning

confidence: 99%

“…Segmental absence of the intestinal musculature (SAIM) is a rare clinicopathological entity characterized by thinning or complete absence of the muscularis propria with preservation of the mucosa [1]. Patients with SAIM usually present with progressive acute abdomen that is most likely associated with intestinal perforation and sepsis.…”

Section: Introductionmentioning

confidence: 99%

“…Patients with SAIM usually present with progressive acute abdomen that is most likely associated with intestinal perforation and sepsis. [1,2] Less commonly, patients may present with more prolonged clinical features such as intolerance to feeding and bilious vomiting [1].…”

Section: Introductionmentioning

confidence: 99%

“…SAIM has been reported in isolated case reports and small series (approximately 20 cases to date), usually associated with prematurity; most cases share presentation within the first 99 days of life [1][2][3][4].…”

Section: Introductionmentioning

confidence: 99%

See 3 more Smart Citations

Segmental Absence of Intestinal Musculature –Presentation in a 10-Year-Old Boy with an Extensive Involved Segment

Athanazio

Rocha

Mattos

et al. 2014

Fetal and Pediatric Pathology

View full text Add to dashboard Cite

Segmental absence of the intestinal musculature is a rare cause of acute abdomen most likely associated with intestinal perforation and sepsis in neonates and adults. We present a case of a 10-year-old boy who developed acute abdomen and was treated with right hemicolectomy and partial resection of the ileum. The ileum showed a 20-cm-long stenotic segment showing prominent thinning of the intestinal wall. This case occurred in an older child, which appears to be rare when comparing the literature. The bowel defect was also the largest described to date, indicating the potential effect of an atonic segment leading to obstructive disease.

show abstract

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

See 2 more Smart Citations

Segmental Absence of Intestinal Musculature –Presentation in a 10-Year-Old Boy with an Extensive Involved Segment

Athanazio

Rocha

Mattos

et al. 2014

Fetal and Pediatric Pathology

View full text Add to dashboard Cite

show abstract

“…The myenteric plexus was not seen in areas of absence of muscle but present where muscular layer was present. Diagnosis of SAIM is made only after pathologic examination of the resected bowel [1]. The usual presentation is consistent with peritonitis, although obstruction may also be a presentation.…”

mentioning

confidence: 99%