Scimitar sign with normal pulmonary venous drainage and anomalous inferior vena cava.

Abstract

(fig 1). Pulmonary scintigraphy showed a substantial decrease in perfusion of the right lung. Echocardiography showed nothing abnormal.A conventional angiogram via the right femoral vein disclosed an infrahepatic interruption of the inferior vena cava with an azygos vein continuation. The supradiaphragmatic examination was non-contributory owing to incom-

Scimitar Syndrome and Azygos Continuation of the Inferior Vena Cava Diagnosed in an Adult-An Unusual Association

“…In addition, interruption of inferior vena cava with azygous continuation was found at computed tomography scan of our patient. Although previously reported, this association is very rare 5,6 …”

“…In addition, interruption of inferior vena cava with azygous continuation was found at computed tomography scan of our patient. Although previously reported, this association is very rare 5,6 After the diagnosis has been correctly established, the presence of a hemodynamically significant left-to-right shunt, recurrent pulmonary infections, and pulmonary sequestration usually represents one of the main indications for surgical correction. 1 The surgical treatment depends upon the anatomy and the presence of other associated cardiac anomalies, and involves partial or total resection of the right lung or redirecting the abnormal vein into the left atrium.…”

Incidental meandering right pulmonary vein, literature review and proposed nomenclature revision

“…Morgan et al [4] described the first case in which the scimitar sign and features of scimitar syndrome were present but the aberrant pulmonary vein ultimately drained normally into the left atrium. Other reported causes of the scimitar sign include an anomalous intrapulmonary venous connection to superior vena cava, obstruction of a major pulmonary vein with development of a distended intrapulmonary collateral and an anomalous IVC with normal pulmonary venous drainage [5,6] .…”

Variants of the scimitar syndrome

“…2 Many terms have been used by a number of authors to describe those cases that, although a close cousin, lack all the elements of the complete scimitar syndrome. 1,[3][4][5][6][7][8][9][10][11][12] There is, however, no general agreement about an exact classification of these variants. In this study, we report our experience of scimitar syndrome variants since 1992.…”