Variants of the scimitar syndrome

Abstract

The heterogeneity of this small series confirms the consistent occurrence of an anomalous arterial supply to the affected lung but considerable variation in pulmonary venous drainage.

Respiratory distress in a 2-month-old infant: Is the primary cause cardiac, pulmonary or both?

“…Scimitar syndrome is a variant of partial anomalous pulmonary venous connection in which part or the entire right lung is drained by right pulmonary veins that connect anomalously to the inferior vena cava or portal veins [ 2 ]. The affected lung and its associated airways, which are drained by the scimitar vein, are often hypoplastic or have unusual bronchial or vascular distribution patterns.…”

A rare case of a patient with aortic root aneurysm, bicuspid aortic valve, and Scimitar syndrome with anomalous venous return to the right superior pulmonary vein

“…Thus, a scimitar vein draining into the left atrium is a rare form of Scimitar variant with only a few cases described in the literature. [5][6][7][8] This condition is called also "meandering pulmonary vein". In this variant of Scimitar syndrome, the meandering pulmonary veinthe anomalous right lower pulmonary vein in our situationhas an abnormal course, which forms the Scimitar sign on chest radiograph, with normal venous return to the left atrium.…”

Coronary venous anatomy and anomalies

“…24 In PAPVR/ TAPVR, pulmonary veins may anomalously drain into the CS which also has an association with unroofed CS. 25,26 Interruption of the inferior vena cava with drainage of the hepatic veins directly to the CS as well as hemiazygous continuation of a left inferior vena cava with drainage into the CS via a persistent left superior vena cava can also lead to CS dilation. 1 A rare condition associated with absence of the CS is Raghib syndrome.…”