Schnitzler syndrome with cold-induced urticaria

Abstract

Schnitzler syndrome is under-recognized, particularly variants of the classical description of Schnitzler syndrome. Other diseases, especially those of hematologic origin, should be ruled out. This condition is largely refractory to conventional therapies, although novel treatments, such as interleukin-1 receptor inhibitor, may show promise.

Schnitzler's syndrome: lessons from 281 cases

“…To date, 281 cases have been reported, with a male–female ratio of 1.5 [2–146]. (Kabashima, Schiff, Frerichs, Van Hoof, Relas, Björk, Fox, Croot: personal communications (p.c.))…”

Chronic Urticarial in Childhood. Clinical Features of Chronic Urticaria in Children. Differential Diagnostics (Part Ii)

“…Известны и другие редкие синдромы, сочетающиеся с крапивницей, такие как синдром Шницлера, Глейча, Макла-Уэлса, но распространенность их в детской популяции низкая [45].…”