Right aortic arch with an aberrant left subclavian artery and aortic coarctation including a descending aortic aneurysm

Abstract

Backround The right aortic arch and aortic coarctation are rare congenital anomalies with the incidence of 0.1% and 0.03–0.04%. We present a case report of a 51-year-old woman with the right aortic arch with aberrant left subclavian artery and coarctation of the aorta with post-stenotic aneurysm. Case presentation Resection of the coarctation and aneurysm with replacement by tubular prosthesis was performed on partial cardiopulmonary bypass via femoral vessels. Conclusion Partial cardiopulmonary bypass is an applicable method for ensuring the perfusion of the distal part of the body and an aberrant left subclavian artery is not a contraindication of this technique.

Systematic review and meta-analysis of right subclavian artery variants and their correlation with cervical-thoracic clinical conditions

“…With a total of 39 included studies, for the 27 studies that had an N > 1, [24–50] the following data were collected: the total number of subjects included in the studies was 41,178 with an average ratio of 1.525:1 regarding the sex of the sample; 12 studies did not indicate the sex of their sample [25,27,31,34,35,37,38,45,47–50] ; one study by Yusuf et al [32] only indicates the sex of the sample that did present the anatomical variant and consisted of 10 men and 17 women, respectively; and, finally, 14 studies [24,26,28–30,33,39–44,46] show that the cumulative data for males was 2964/5393, which is equivalent to 54.9%, and cumulative data for females was 2429/5393, which is equivalent to 45.1%. Finally, regarding the geographical distribution of the included studies, [24–50,53–64] in 13 studies, the sample was European, which is equivalent to 33.3% of the included studies; in 12 studies, the sample was from North America, which is equivalent to 30.8% of the included studies; and, finally, 14 studies had a sample from Asia, which is equivalent to 35.9% of the studies included in this review (Table 2).…”

“…Does not present USA 10 patients. 1 male 9 female Middle ages: 48 ± yr Chen et al 2021 [31] Retrospective study (13, Behram et al 2021 [27] Retrospective study (11, [32] Retrospective study (7513) Retroesophageal ARSA in 27 exams (0.36%, 95% CI: 0.22%-0.50%) [59] Case study ARSA with course to the right between the trachea and the esophagus 100% incidence Does not present India 1 male Age: 35 yr Sadeghian et al 2020 [62] Case study ARSA with dysphagia 100% incidence Does not present USA 1 male Age: 52 yr Sabol et al 2019 [60] Case study Right aortic arch, aberrant left subclavian artery aortic coarctation 100% incidence Does not present Slovakia 1 female Age: 51 yr Sabljak et al 2011 [56] Case study Hypopharyngeal and cervical esophageal carcinoma with coexistence of ARSA 100% incidence Does not present Serbia 1 female Age: 65 yr Pramesh et al 2003 [53] Case study Esophageal carcinoma with coexistence of ARSA 100% incidence Does not present India 1 female Age: 52 yr Muraoka et al 2017 [33] Retrospective study (10) Aberrant left subclavian artery with or without stenosis 100% incidence Does not present Japan 10 fetuses: 6 male 4 female Age: 24-39 wk (Continued )…”

Surgical Management of Right Aortic Arch Obstruction Associated With Rare Form of Vascular Ring

“…Cardiopulmonary bypass was used to provide hemodynamic stability, allowing enough time and exposure for the anastomoses. 3 Use of the left ventricular vent is optional and depends on surgical team preferences. We are aware that the extra-anatomical bypass grafting is far from a perfect method for children with aortic arch pathology.…”

Aberran Subklavi̇an Arteri̇n Morfoloji̇k Ve Kli̇ni̇k Yönleri̇:tek Merkezli̇ Çkbt Tabanli Çalişma

“…Aberrant left subclavian artery (ALSA), which is a more rare ASA anomaly, usually accompanies the right aortic arch (RAA). In the literature, the prevalence of RAA has been reported to be 0.1% in the adult group and is a rare entity 2,3 . Although patients with ASA anomalies are generally asymptomatic, patients may rarely cause dysphagia, dyspnea, cough and recurrent aspirations 4 .…”