Retroperitoneal lymphangioma: an unusual location and presentation

Abdominal lymphangioma in children: Report of three cases

“…3,11 However, complicated cases present as acute abdomen which usually requires surgical intervention, although an emergency operation is not always necessary. In case 3, for instance, the abdominal pain improved with conservative therapy with antibiotics, but the abdominal distension became exacerbated.…”

“…The incidence of abdominal lymphangiomas is unknown; however, they account for from 3% 1 to 9.2% 2 of all pediatric lymphangiomas, with retroperitoneal lymphangioma representing less than 1% of abdominal lymphangiomas. 3 From 50% to 60% of cystic lymphangioma cases present symptoms by age 1 year and 90% of the cases present by age 2 years. 3 Abdominal cystic lymphangiomas arise from the mesentery (59%-68%), omentum (20%-27%), and retroperitoneum (12%-14%), 4,5 and most clinical presentations are due to mesenteric lymphangiomas.…”

“…Although abdominal lymphangiomas usually present with no clinical symptoms and retroperitoneal lymphangiomas are usually diagnosed in older children and adults, 3 complicated cases have been reported. Cases of abdominal lymphangioma present acute abdomen attributed to intestinal obstruction 1 with volvulus, 6 extrinsic compression and entrapment or peritonitis caused by rupture, 7 torsion, hemorrhage into the cyst, 8 or an infected cyst.…”

A rare case of abdominal lymphangioma masquerading an adenaxal mass

“…After birth, they can become markedly dilated as a result of both the collection of fluid and the budding of pre-existing spaces. 2 The other explanations for the origin of lymphangioma include obstruction of lymph channels secondary to fibrosis, inflammation, trauma, node degeneration; or failure of endothelial secretory function, which explains the pathophysiology of this in adults. Not only these are such rare entity, but they also pose diagnostic challenges to clinician, that is the reason we found this case worthy of reporting to the medical fraternity.…”

A huge lymphovenous malformation in the retroperitoneum

“…It has been reported that retroperitoneal lesions account for approximately 1% of all lymphatic malformations [6,7]. Actual prevalence of retroperitoneal lymphovenous malformation is unclear for the reason that asymptotic cases might be missed, and differentiating lymphovenous malformations from hemangiomas is sometimes confusing clinically.…”