Restrictive cardiomyopathy in an infant with massive biatrial enlargement and normal ventricular size and pump function

Abstract

Restrictive cardiomyopathy in an infant with massive biatrial enlargement and normal ventricular size has been reported only once previously [3]. We now present a 13-month-old patient with severe and progressive congestive heart failure who demonstrated normal ventricular cavity size with biatrial enlargement. Ejection fraction and echocardiographic ventricular function studies were normal.

Massive dilatation of the atria and coronary sinus in a child with restrictive cardiomyopathy and persistence of the left superior vena cava

“…experience, autopsy permission was not granted so that the pathologic anatomy and histology is not known. The common feature in the pediatric patients has been massive biatrial enlargement on EKG, on chest roentgenogram [2][3][4], and by echo [3]. This has not been a consistent finding in the adult population [6].…”