Malignant perip heral nerv e shea th tumors of the nos e and paranasal sinuses are extreme ly uncomm on. We report the case ofa 65-y ear-old woman who presented with a rapid emergence of "nasal polyps " that comp letely obstructed her nasalpassag es. Six years earliet; she hadbeen asse ssed else where f or nasal polyps. A t presentation, the patient exhibited grosspolypo sis, with lesionsprotrudingfrom both nostrils. Histology confirmed a diagnosis ofa malignant periph eralnerve sheath tumor: This case demonstrates that symp toms ofnasal obstruction are not always secondary to simp le causes. We discuss the clinical pi cture ofnasal and paranasalmalignant p eriph eralnerve shea th tumor; its pathology, and its treatm ent.