Facial malignant peripheral nerve sheath tumors

Martin-Duverneuil, N; Auriol, M; Béhin, Anthony; Bertrand, Jacques-Charles; Chiras, J.

doi:10.1016/s0150-9861(06)77269-8

Cited by 9 publications

(10 citation statements)

References 35 publications

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“…Malignant schwannoma, also called neurofibrosarcoma, neurogenic sarcoma or malignant tumor of the peripheral nerve sheath (malignant peripheral nerve sheath tumors: MPNSTs), is a tumor of the peripheral nervous system that develops in the nerve sheath at the expense of Schwann cells [1]. This tumor is rare with an estimated incidence of 0.1 per 100,000 per year in the general population [1, 2].…”

Section: Discussionmentioning

confidence: 99%

“…This tumor is rare with an estimated incidence of 0.1 per 100,000 per year in the general population [1, 2]. …”

Section: Discussionmentioning

confidence: 99%

“…Malignant schwannomas or neurofibrosarcomas are rare nerve tumors with very poor prognosis; maxillofacial locations are very exceptional [1]. These tumors may be either primitive or as a complicating part of neurofibromatosis type 1 (NF-1), also known as von Recklinghausen’s neurofibromatosis [1].…”

Section: Introductionmentioning

confidence: 99%

“…These tumors may be either primitive or as a complicating part of neurofibromatosis type 1 (NF-1), also known as von Recklinghausen’s neurofibromatosis [1]. We report an exceptional case of malignant schwannoma of the infratemporal fossa discovered at a late evolving stage, with a large extension to the neighboring structures, and discuss, through a literature review, the various features of this tumor.…”

Section: Introductionmentioning

confidence: 99%

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Malignant schwannoma of the infratemporal fossa: a case report

et al. 2015

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IntroductionMalignant schwannomas or neurofibrosarcomas are rare nerve tumors of unknown etiology. These neoplasms are highly aggressive with a marked propensity for local recurrence and metastatic spread. Their management continues to be a challenge for pathologists and surgeons. Maxillofacial locations are very exceptional. We report the case of a patient with unusual malignant schwannoma of the infratemporal fossa discovered at a late evolving stage.Case presentationA 56-year-old woman, of Moroccan nationality, presented to our hospital in 2013 with a large right-sided hemifacial swelling that had evolved over the previous 4 months, with a limitation of mouth opening, nasal obstruction and episodes of epistaxis. A CT scan and MRI showed a large and invasive tumor occupying her right infratemporal fossa and maxillary sinus, with sphenoidal, ethmoidonasal, nasopharyngeal and intraorbital extension. A nasal endoscopic biopsy was performed. Immunohistochemical examination concluded a diagnosis of malignant schwannoma, and a palliative radiotherapy was decided; however, our patient died 10 days later.ConclusionsMalignant schwannoma of paranasal sinuses and the anterior skull base is a rare tumor that involves a high rate of local invasion. The prognosis is poorer compared to that occurring in the trunk and extremities.

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Section: Discussionmentioning

confidence: 99%

“…This tumor is rare with an estimated incidence of 0.1 per 100,000 per year in the general population [1, 2]. …”

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

See 2 more Smart Citations

Malignant schwannoma of the infratemporal fossa: a case report

et al. 2015

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“…Tumours arise from Schwann cells or perineural cells that ensheath axons and extend along neural tracts. They are aggressive cancers that have high rates of recurrence and a poor prognosis (3). Occurrence in the head and neck region has been shown to be a predictor of adverse outcome.…”

Section: Introductionmentioning

confidence: 99%

Malignant peripheral nerve cell sheath tumour of the upper lip: a rare case

Ward

Bhatt

Barnard

2010

Journal of Surgical Case Reports

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Unilateral widening of the inferior alveolar nerve canal: a rare anatomic variant mimicking disease

et al. 2012

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We report a case of an asymptomatic healthy 49-year-old male patient with an incidental finding of enlargement of the right inferior alveolar nerve (IAN) canal (9 vs. 4 mm). After 2 years, follow-up magnetic resonance imaging (MRI) revealed no change in the findings. In addition, MR-based diffusion tensor imaging with tractography of the right and left mandibular nerves showed that the difference in size between the right and left nerves was caused by an increased number of nerve fibers in the right IAN. During the entire follow-up period of 4 years, the patient remained symptom-free. Therefore, we suggest that the enlargement in our patient was a pure anatomic variant. However, a multitude of conditions are known to produce the identical radiological appearance in conventional radiology, including benign and malignant tumors, vascular malformations, and inflammatory disorders. We describe these pathologies in more detail as well as the possibilities for examinations with different MRI sequences.

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Facial malignant peripheral nerve sheath tumors

Cited by 9 publications

References 35 publications

Malignant schwannoma of the infratemporal fossa: a case report

Malignant schwannoma of the infratemporal fossa: a case report

Malignant peripheral nerve cell sheath tumour of the upper lip: a rare case

Unilateral widening of the inferior alveolar nerve canal: a rare anatomic variant mimicking disease

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