Rare Desmoplastic Fibroma in Ramus and Mandibular Angle: Presentation of a Case Report With Review of Literature

Abstract

Desmoplastic fibroma is a rare, benign fibrous tumor of bone which is locally aggressive. The mandible is the most prevalent affected of the facial bones. Nevertheless, reports of desmoplastic fibroma affecting the mandible are seldom in the literature. It causes bone destruction and has a high tendency for local recurrence. In this case report, we report a case of desmoplastic fibroma which is located in mandibular angle and extended to coronoid process, in 20-year-old female patient.
 © 2019 Tehran University of Medical Sciences. All rights reserved.
 Acta Med Iran 2019;57(7):456-460.

Periosteal reaction as a crucial radiographic finding for desmoplastic fibroma of the jaw bone in children: A case report

“… 10 15 Rapid expansion and subsequent cortical perforation can also result in the initiation of new bone formation from an osteogenic layer of periosteum, producing a sunburst appearance. 6 9 11 Similarly, in the present case, bony spicules as an indicator of a periosteal reaction arising from the cortical plates of the mandible were visible, and layering bone formation in the labial cortex was also seen. Since the periosteal reaction originates from the periosteum, it may present only as fine spicules on conventional radiography in the initial stages, as seen in the present case and also in the case reported by Dalili-Kajan et al, 11 Khatib and Pogrel., 15 Said-Al-Naief et al, 16 and Shi et al 17 …”

“… 10 Diagnosis at older ages may reflect late recognition. An equal sex distribution has been reported in most studies, 3 6 11 but Wood et al 9 stated there was a female predilection (56%). The most common clinical feature of desmoplastic fibroma of the jaw bones is painless swelling; the others include facial asymmetry, tooth displacement and mobility, trismus, and pathological fractures, 3 4 6 7 12 although the latter is more common in long bones.…”

“…The mandible is the most common site of involvement in the craniofacial region, mainly in the posterior region (ramus, angle, and molar area), followed by long bones and the pelvis. 3 5 6 7 Causative links with trauma and endocrine or genetic factors have been suggested in the literature, but the etiology of desmoplastic fibroma remains unknown. 8 Asymptomatic swelling followed by tooth displacement and mobility could be considered the most representative clinical findings.…”

“…8 Asymptomatic swelling followed by tooth displacement and mobility could be considered the most representative clinical findings. 6 …”

“…Although most authors reported the occurrence of desmoplastic fibroma in patients younger than the third decade of life, 4 6 9 some reports described a broader age range, from 6 months to 60 years at the time of diagnosis. 10 Diagnosis at older ages may reflect late recognition.…”