Raeder Paratrigeminal Neuralgia Evolving to Hemicrania Continua

Porzukowiak, Tina Renae

doi:10.1097/opx.0000000000000524

Cited by 3 publications

(3 citation statements)

References 24 publications

(23 reference statements)

Supporting

Mentioning

Contrasting

Order By: Relevance

“…(i) Both headache disorder existing simultaneously: CH is the most common associated headache with HC. [ 50 51 ] Other reported headaches are migraine,[ 52 ] TTH,[ 53 ] trochlear headache,[ 54 ] sexual headache,[ 55 ] and trigeminal neuralgia,[ 56 ] (ii) other primary headache orders evolving into HC: there are case reports where CH,[ 57 ] PH,[ 58 ] SUNCT,[ 59 ] migraine,[ 60 ] and Raeder syndrome[ 61 ] have evolved into HC, (iii) HC evolving into other primary headaches: there are two such cases where HC have transformed into other headaches (PH and LASH syndrome). [ 62 ]…”

Section: Ifferential D Iagnosismentioning

confidence: 99%

Hemicrania continua

Prakash¹,

Adroja²

2018

Ann Indian Acad Neurol

View full text Add to dashboard Cite

Hemicrania continua (HC) is an indomethacin responsive primary chronic headache disorder which is currently classified as a subtype of trigeminal autonomic cephalalgias (TACs). It is not very uncommon. There are >1000 cases of HC in the literature, and it constitutes 1.7% of total headache in the clinic settings. Misdiagnosis for HC is very common at all clinical settings. A diagnosis of HC is missed even by neurologists and headache specialists. It is characterized by a continuous strictly unilateral headache with superimposed exacerbations. Just like other TACs, exacerbations are associated with cranial autonomic symptoms and restlessness. A large number of patients may have migrainous features (nausea, vomiting, photophobia, and phonophobia) during exacerbations phase. The “key” feature of HC is persistent featureless background headaches. However, patients and physicians may focus only on the exacerbation part. As durations, frequency and associated symptoms of exacerbations are highly variables; it may mimic a large number of primary and secondary headache disorders. Migraine and cluster headache are two most common misdiagnosed conditions. Another specific feature of HC is remarkable repose to indomethacin. A “complete” response to indomethacin is as “sine qua non” for HC. However, a few other medications may also be effective in a subset of HC patients. Various surgical procedures have been tried with mixed results in patients who were intolerant to indomethacin or other drugs.

show abstract

Section: Ifferential D Iagnosismentioning

confidence: 99%

Hemicrania continua

Prakash¹,

Adroja²

2018

Ann Indian Acad Neurol

View full text Add to dashboard Cite

show abstract

“…Raeder's syndrome can be misdiagnosed as hemicrania continua or paroxysmal hemicrania and vice versa. It is important to perform a trial of indomethacin, which is usually not helpful in Raeder's syndrome (31), although the transition of Raeder's syndrome into indomethacin responsive hemicranias continua has been described (32). The response to indomethacin to such pain syndromes is however unspecific (33).…”

Section: Diagnostic Considerationsmentioning

confidence: 99%

“…Most cases of idiopathic Raeder's syndrome were self-limiting or responded to steroids. One case of successful treatment with onabotulinumtoxin A was published (31).…”

Section: Treatmentmentioning

confidence: 99%

Facial pain: Overlapping syndromes

Evers

2017

Cephalalgia

View full text Add to dashboard Cite

Premise This review summarises the pain syndromes that overlap between headache and facial pain and overlap between pain and cranial nerve lesion. Problem These syndromes share two features in common. First, they show both cranial nerve impairment (e.g. palsy, autonomic dysfunction) and pain; second, they have inflammatory (and/or small vessel) processes as the underlying mechanism. A typical representative of these syndromes is recurrent painful ophthalmoplegic neuropathy, which was previously called ophthalmoplegic migraine and was regarded as a migraine subtype. It is now supposed that this syndrome is caused by an inflammation of one of the ocular motor nerves. Other syndromes discussed in this review are optic neuritis, Tolosa-Hunt syndrome, ischaemic ocular motor nerve palsy, and the very rare Raeder's syndrome. Treatment of all these syndromes is mainly based on steroids. Potential solution Management of possibly underlying disorders such as multiple sclerosis or atherosclerosis should also be considered.

show abstract

Hemicrania continua: clinical review, diagnosis and management

Prakash¹,

Patel

2017

JPR

View full text Add to dashboard Cite

Hemicrania continua (HC) is an indomethacin-responsive primary headache disorder which is currently classified under the heading of trigeminal autonomic cephalalgias (TACs). It is a highly misdiagnosed and underreported primary headache. The pooled mean delay of diagnosis of HC is 8.0 ± 7.2 years. It is not rare. We noted more than 1000 cases in the literature. It represents 1.7% of total headache patients attending headache or neurology clinic. Just like other TACs, it is characterized by strictly unilateral pain in the trigeminal distribution, cranial autonomic features in the same area and agitation during exacerbations/attacks. It is different from other TACs in one aspect. While all other TACs are episodic, HC patients have continuous headaches with superimposed severe exacerbations. The central feature of HC is continuous background headache. However, the patients may be worried only for superimposed exacerbations. Focusing only on exacerbations and ignoring continuous background headache are the most important factors for the misdiagnosis of HC. A large number of patients may have migrainous features during exacerbation phase. Up to 70% patients may fulfill the diagnostic criteria for migraine during exacerbations. Besides migraine, its exacerbations can mimic a large number of other primary and secondary headaches. The other specific feature of HC is a remarkable response to indomethacin. However, a large number of patients develop side effects because of the long-term use of indomethacin. A few other medications may also be effective in a subset of patients with HC. Various surgical interventions have been suggested for patients who are intolerant to indomethacin. Several aspects of HC are still not defined. There is a great heterogeneity in types of patients or articles on the HC in the literature. Diagnostic criteria have been modified several times over the years. The current diagnostic criteria are too restrictive in some aspects. We suggest a more accommodating type of criteria for the appendix of International Classification of Headache Disorder (ICHD).

show abstract

Raeder Paratrigeminal Neuralgia Evolving to Hemicrania Continua

Cited by 3 publications

References 24 publications

Hemicrania continua

Hemicrania continua

Facial pain: Overlapping syndromes

Hemicrania continua: clinical review, diagnosis and management

Contact Info

Product

Resources

About