Pyloroduodenal deformity due to liver malformation associated wtih omphalocele

Giant omphalocele, intrinsic duodenal obstruction

“…This complication may be corrected by either gastrojejunostomy or, in some cases, conservative management with gastric decompression by an indwelling feeding tube. 5,6 Our cases show that intrinsic obstruction of the duodenumFatresia or webFcan also occur in patients with giant omphaloceles. Differentiation of intrinsic from extrinsic duodenal obstruction is important so that appropriate treatment can be started early.…”

“…The prior duodenal obstructions reported in giant omphaloceles have been extrinsic obstructions due to a malformed liver. 5,6 This type of obstruction is presumably caused by an abnormal growth of the caudate lobe of the liver around the antropyloric region, allowed by the extracorporeal location of both. This complication may be corrected by either gastrojejunostomy or, in some cases, conservative management with gastric decompression by an indwelling feeding tube.…”