Primary retroperitoneal cavernous hemangioma: An exceptional disease in adulthood

Abstract

Primary retroperitoneal cavernous hemangioma is an extremely rare disease in clinical practice. It is classified as a vascular tumor. Only three cases have been reported in the literature. The diagnosis is uncommon due to the lack of specific radiological features. It becomes symptomatic as a consequence of its enormous size or complications like rupture or compression. We herein report a unique case of primary retroperitoneal cavernous hemangioma treated with conventional surgery in a 35‐year‐old male patient admitted to our department for chronic abdominal pain. Retroperitoneal cavernous hemangioma is an extremely rare vascular tumor in adulthood. Confirmation is made by histopathological examination after total surgical resection.

Retroperitoneal capillary arteriovenous malformation mimicking a malignant neoplasm

“…4,10,11 They are typically attached or adjacent to surrounding organs or major vessels. 5,6,[8][9][10][12][13][14][15] In contrast, in the present case, the lesion formed a capsule that was separated from other organs and major vessels, similar to a neoplasm. Surgical resection is possible for diagnostic and therapeutic purposes, although intervention for vascular malformations is indicated only for large lesions with a threat of incidental rupture and/ or bleeding.…”

“…On imaging studies, cavernous hemangiomas are often characterized by a lobulated septate mass without a clear capsule (cotton wool appearance) 4,10,11 . They are typically attached or adjacent to surrounding organs or major vessels 5,6,8–10,12–15 . In contrast, in the present case, the lesion formed a capsule that was separated from other organs and major vessels, similar to a neoplasm.…”

“…In previous reports, 4–15 retroperitoneal vascular malformations affected patients of all ages; approximately half were 20–40 years old. No obvious bias was observed in sex or laterality.…”

“…Vascular tumors and malformations in the retroperitoneal space are rare, with fewer than 30 cases reported in the English literature 4–15 . Among them, the most prevalent is venous malformation, including cavernous hemangioma.…”

Retroperitoneal venous malformation mimics paraganglioma on triple imaging modalities

“…The pathology description strongly indicates a venous malformation. Venous malformations are benign congenital vascular anomalies that can arise in various organs such as the liver, spleen, kidneys, adrenal glands and even intramuscularly 7. According to the International Society for the Study of Vascular Anomalies classification, they are one of two vascular anomalies, with the other being vascular tumours like infantile haemangiomas 8.…”