Pigmentation in the Bloch-Sulzberger Syndrome (Incontinentia Pigmenti)

A Case of Incontinentia Pigmenti

“…That disorder may he regarded as caused by " incontinentia pigmenti" , this means by the inability of the basal cells to hold and metabolize melanin. Most authors believe the pigmentations to be postinflammatory, preceded by the papular and vesicular eruptions of the early stages, and therefore similar to those seen in lichen planus, Riehl's melanosis, parapsoriasis and many other skin diseases [27,28]. Japanese investigators, however, reported hyperpigmentation appearing before or beside bullae.…”