Peculiar facial erythematosquamous lesions in two siblings with cyclical summer improvement and winter relapse: A variant of keratosis lichenoides chronica?

Arata, Jirô; Senô, Akemi; Tada, Jôji; Wada, Emi; Tamaki, Hiroyuki; Tamaki, Miwako

doi:10.1016/0190-9622(93)70121-9

Cited by 18 publications

(12 citation statements)

References 4 publications

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“…However, a spontaneous resolution has recently been reported ] 10, 11]. Our patient experienced spontane ous improvements of the disease in summer after exposures to sunlight, as in the patients reported by Lang [12], Arata [17] andTorrelo [11].…”

Section: Discussionsupporting

confidence: 77%

“…Only 2 of previously reported pediatric cases of KLC [11,13] have findings very similar to those of our patient. In addition, the 2 siblings described by Arata et al [17] may represent a peculiar variant of KLC limited to the face. In contrast, many unusual features (congenital familial syn drome, diffuse ichthyosiform dermatosis, diffuse palmoplantar keratoderma, absence of lichenoid tissue reaction on histologic examination) were present in the patient reported by Barrière et al [14]; this latter case failed to fulfil the three hallmarks essential for the diagnosis of KLC.…”

Section: Discussionmentioning

confidence: 97%

“…Reports of KLC are particularly rare in childhood [11,13,14,17]. Braun-Falco et al [8] in their review reported as many as 5 cases out of 37 with onset before 10 years of age.…”

Section: Discussionmentioning

confidence: 99%

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Keratosis lichenoides chronica: A Pediatric Case

et al. 1995

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Keratosis lichenoides chronica (KLC) is a rare chronic disorder of keratinization characterized by lichenoid hyperkeratotic papules arranged in a linear pattern, erythematosquamous plaques and seborrhea-like dermatitis on the face. Adults between 20 and 50 years of age are usually affected, but the disease is very uncommon in childhood. Our purpose was to study the clinical and histopathologic findings and course of KLC in one pediatric case. Detailed clinical data were studied. Two punch biopsies were performed and histopathologic features were compared with those of other reported cases of KLC. In our patient, a 4-year-old boy, the clinical features of the lesions did not deviate notably from those of other cases of KLC. The histologic pattern of the papules was typical of KLC, while that of the erythematosquamous plaques showed some dyskeratotic keratinocytes. The histologic pattern of the erythematosquamous lesions is peculiar in our case, whereas only a nonspecific pattern is reported in the literature. The papular and erythematosquamous lesions showed similar histopathologic features suggesting that they could be different degrees of evolution of the same lesion.

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Section: Discussionsupporting

confidence: 77%

Section: Discussionmentioning

confidence: 97%

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Keratosis lichenoides chronica: A Pediatric Case

et al. 1995

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“…Some case reports remain difficult to classify consider ing the available data [47,48] or unique clinical and histo logical features [49][50][51].…”

Section: Unclassifiedmentioning

confidence: 99%

Keratosis lichenoides chronica: The Centenary of Another Kaposi’s Disease

Masouyé

Saurat²

1995

Dermatology

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In 1895, Kaposi used the term ‘lichen ruber acuminatus verrucosus et reticularis’ to describe the case of a 27-year-old woman with a linear, warty lichenoid eruption. We have reviewed the literature and found 50 cases, of which only 40 had common features reminiscent of the original description of Kaposi. These ‘authentic’ cases of keratosis lichenoides chronica (KLC) showed strong clinical and histological similarity, a uniformity indicating that KLC is an entity and is distinct from lichen planus. KLC may be associated with internal diseases such as glomerulonephritis and lymphoproliferative disorders.

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“…Th e rarity of pediatric cases may be due to late diagnosis, rather than actual low incidence among children (90). KLC rarely aff ects several persons from the same family (59,106); only 10 (8.70%) cases have been reported so far, all being aff ected in childhood, while congenital cases were described only in 4 (3.48%) patients (Table 3). Table 3 shows that KLC lesions are most commonly found on the extremities, both in children and adults, whereas 40% of patients present with palmoplantar hyperkeratosis; facial lesions are more common in adults than in children; nail lesions are more common in adults, aff ecting over 30% of patients, presenting as yellow discoloration, thickening and longitudinal ridging of the nail plate and nail bed hyperkeratosis; oral lesions are more common in adults than in children; ocular lesions include blepharitis, conjunctivitis, anterior uveitis and iridicyclitis which aff ect both children and adults; genital lesions, including keratotic papules on the scrotum and penis, chronic balanitis and phimosis, have been reported in 9.88% of adults, but in children they have not been described; pruritus occurs in less than 20% of patients, both in children and adults (Table 3).…”

Section: Resultsmentioning

confidence: 99%

Keratosis Lichenoides Chronica – a Case Report and Literature Review

Paravina

Cvetanović²,

Kostov³

et al. 2014

Serbian Journal of Dermatology and Venereology

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linear and reticular red to purple papules with white scaly surface. Before the appearance of skin lesions, the patient's history was unremarkable and he denied taking any medications. He was treated under the diagnosis of psoriasis vulgaris, and lichen verrucosus. In 2014, he underwent phimosis surgery. Th ere was no family history of skin conditions. ExaminationOn admission, the patient presented with symmetrical generalized eruptions of erythemolivid to dark livid papules and nodules with a keratotic surface, in a solitary, linear or reticular pattern on the lower lateral parts of the trunk and along the extremities ( Figures 1-3); the infi ltrated lesions were prominent, verrucous and hyperkeratotic. Mild erythematosquamous lesions were present on the face. Solitary erythematous papules on erythematous base T he idea for this paper on keratosis lichenoides chronica (KLC) was born after the fi rst visit of a patient with an unusual clinical picture resembling both psoriasis and lichen planus, but also distinct from them, posing a diagnostic and therapeutic dilemma. After a consultation with Prof. Danilo Stevanović, whom we hereby wish to thank, and repeated histopathological examinations, the diagnosis of keratosis lichenoides chronica was confi rmed. Papers of Böer (1) Case report Case historyWe report a 40-year old man who developed skin lesions on the trunk and extremities more than 10 years earlier: asymptomatic, symmetrically distributed AbstractKeratosis lichenoides chronica represents a distinct entity, a rare disease of unknown etiology and pathogenesis, with clinical manifestations which, although typical, require extensive differential diagnosis. The course of the disease is chronic, progressive, and it is resistant to various treatment options, so despite variations in the clinical picture it is really easier to diagnose than to treat. This is a case report of a male patient in whom the diagnosis of keratosis lichenoides chronica was based on typical clinical picture, repeated biopsies and histopathological findings, course of the disease and poor response to any therapy.

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Peculiar facial erythematosquamous lesions in two siblings with cyclical summer improvement and winter relapse: A variant of keratosis lichenoides chronica?

Cited by 18 publications

References 4 publications

Keratosis lichenoides chronica: A Pediatric Case

Keratosis lichenoides chronica: A Pediatric Case

Keratosis lichenoides chronica: The Centenary of Another Kaposi’s Disease

Keratosis Lichenoides Chronica – a Case Report and Literature Review

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