PEComa of the urinary bladder

Shringarpure, Sanish S; Thachil, Joseph V; Menon, Maya

doi:10.4103/1319-2442.100943

Cited by 11 publications

(6 citation statements)

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“…A search of the English literature indicated that only 12 previous cases of PEComas of the urinary bladder have been reported thus far [11-20], whereas two cases mentioned in Chinese-language literatures with English-language abstract were excluded because of the unavailable detail information [21,22]. The clinicopathologic features of all published cases of this kind of lesion are summarized in Table 1.…”

Section: Discussionmentioning

confidence: 99%

“…To date, non-AML/non-LAM/non-CCST PEComas have progressively been documented in a variety of anatomical sites, such as visceral organs, soft tissue and bone [3-10]. However, only 12 cases of PEComas of the urinary bladder have been documented in the English-language literature worldwide [11-20]. Herein, we present a urinary bladder lesion occurring in a Chinese adolescent.…”

Section: Introductionmentioning

confidence: 99%

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Perivascular epithelioid cell neoplasm of the urinary bladder in an adolescent: a case report and review of the literature

Liu

Chen

et al. 2012

Diagn Pathol

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Perivascular epithelioid cell neoplasms (PEComas) of the urinary bladder are extremely rare and the published cases were comprised predominantly of middle-aged patients. Herein, the authors present the first urinary bladder PEComa occurring in an adolescent. This 16-year-old Chinese girl present with a 3-year history of abdominal discomfort and a solid mass was documented in the urinary bladder by ultrasonography. Two years later, at the age of 18, the patient underwent transurethral resection of the bladder tumor. Microscopically, the tumor was composed of spindled cells mixed with epithelioid cells. Immunohistochemically, the tumor were strongly positive for HMB45, smooth muscle actin, muscle-specific actin, and H-caldesmon. Fluorescence in situ hybridization analysis revealed no evidence of EWSR1 gene rearrangement. The patient had been in a good status without evidence of recurrence 13 months after surgery. Urinary bladder PEComa is an extremely rare neoplasm and seems occur predominantly in middle-aged patients. However, this peculiar lesion can develop in pediatric population and therefore it should be rigorously distinguished from their mimickers.Virtual slidesThe virtual slide(s) for this article can be found here: http://www.diagnosticpathology.diagnomx.eu/vs/1870004378817301

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Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Perivascular epithelioid cell neoplasm of the urinary bladder in an adolescent: a case report and review of the literature

Liu

Chen

et al. 2012

Diagn Pathol

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“…Angiomyolipoma belongs to a family of neoplasms called perivascular epithelioid cell tumors (PEComas) [1][2][3][4][5][6][7][8]. The World Health Organization (WHO) defines PEComas as ''mesenchymal tumors composed of histologically, ultra structurally, and immunohistochemically distinctive perivascular epithelioid cells C [9].…”

Section: Introductionmentioning

confidence: 99%

Angiomyolipoma of the kidney: Clinicopathological and immunohistochemical study

Esheba

2013

Journal of the Egyptian National Cancer Institute

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“…The management has been variable, but local resection appears to be curative for patients with benign tumours. A few patients were managed with TURBT alone and did not require further surgical intervention 7 8 11. There are several reports of PEComas of the bladder treated successfully with partial cystectomy 7 10 12 13 17 18 21.…”

Section: Discussionmentioning

confidence: 99%

Perivascular epithelioid cell tumour of the bladder

et al. 2014

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SUMMARYA 39-year-old woman presented with a long history of pelvic pain and urinary urgency. Prior workup by her primary care doctor had been negative. The patient's gynaecologist ultimately referred her to a urologist following an ultrasound that revealed a possible bladder mass. MRI of the abdomen and pelvis demonstrated a 4 cm soft tissue lesion arising from the bladder. Cystoscopy showed an atypical mass on the anterior bladder wall, and pathological examination of the TURBT (transurethral resection of the bladder tumour) specimen revealed a perivascular epithelioid cell tumour (PEComa) with involvement of the detrusor muscle. The patient underwent a robotically assisted laparoscopic partial cystectomy. Final pathology confirmed a PEComa with negative margins. The patient had an uncomplicated postoperative course and is doing well following surgery. A surveillance cystoscopy at 6 months showed no evidence of recurrence. This case underscores the variability of clinical presentation of PEComas while proposing an appropriate method of surgical management. BACKGROUND

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PEComa of the urinary bladder

Cited by 11 publications

References 0 publications

Perivascular epithelioid cell neoplasm of the urinary bladder in an adolescent: a case report and review of the literature

Perivascular epithelioid cell neoplasm of the urinary bladder in an adolescent: a case report and review of the literature

Angiomyolipoma of the kidney: Clinicopathological and immunohistochemical study

Perivascular epithelioid cell tumour of the bladder

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