Parry Romberg Syndrome with localized scleroderma: a case report

Khan, Muhammad Amjad; Negi, R. S.; Gupta, Nikita

doi:10.4317/jced.51409

Cited by 22 publications

(35 citation statements)

References 13 publications

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“…Neurological disorders including migraine, trigeminal nerve palsy and epilepsy occur in 20%, and ophthalmological complications in 15% of patients [25]. Sometimes the disease is associated with hair loss and premature greying [24]. Maxillary deformity may develop in a proportion of cases, manirozpoczyna się głównie u dzieci poniżej 10. roku życia, ale może pojawić się w każdym wieku [23].…”

Section: Twardzina Linijnaunclassified

“…Charakteryzuje się zanikiem połowy twarzy (nieco częściej lewej strony), który obejmuje skórę, tkankę podskórną i kości (ryc. 7 A-C) [10,24]. Asymetria twarzy jest szczególnie wyraźna, gdy choroba ma początek w wieku dziecięcym i hamuje prawidło-we kształtowanie zajętych struktur (ryc.…”

Section: Twardzina Linijnaunclassified

“…Mixed form of localized scleroderma diagnosed in approximately 15% of patients (mostly children) and characterized by a combination of ≥ 2 varieties do utraty włosów na głowie oraz ich przedwczesnego siwienia [24]. W części przypadków występu-je deformacja szczęki, co objawia się atrofią korzeni zębowych, opóźnionym wyrzynaniem zębów oraz wadami zgryzu [3].…”

Section: Mixed Form Of Localized Sclerodermaunclassified

“…the dermis, subcutaneous tissue and underlying bone (Figs. 7 A-C) [10,24]. Facial asymmetry is particularly prominent when the disease begins in childhood and inhibits normal development of the affected structures (Fig.…”

Section: Twardzina Linijnamentioning

confidence: 99%

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Localized scleroderma – classification and tools used for the evaluation of tissue damage and disease activity/severity

Wolska-Gawron¹,

Krasowska²

2017

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Localized scleroderma is a rare autoimmune disorder affecting the dermis, subcutaneous tissue and deeper structures. The course of localized scleroderma includes three stages: early inflammation, progressive sclerosis and atrophy. The active stage of the disease is characterized by erythema ('lilac ring'), skin induration, and appearance of new or expansion of pre-existing skin lesions during the preceding month. The most recent localized scleroderma classification recognizes five types of the disease: localized, generalized, linear, deep and mixed. Various methods have been proposed for the evaluation of disease activity or severity and tissue damage, including ultrasonography, thermography, durometry, computed tomography and magnetic resonance imaging. However, all of them have their limitations, as they only make it possible to assess one component of the disease: activity or severity or tissue damage. The LS Cutaneous Assessment Tool (LoSCAT) questionnaire is a promising method of patient evaluation because of its availability, repeatability of results and sensitivity to changes resulting from treatment. STRESZCZENIETwardzina ograniczona jest rzadką chorobą autoimmunologiczną, która przebiega z zajęciem skóry, tkanki podskórnej i tkanek głębiej położonych. Choroba klinicznie ma trzy fazy: wczesną zapalną, postępującego stwardnienia i zanikową (atroficzną). Wykładnikami aktywnego procesu chorobowego są: rumień (lilac ring), stwardnienie skóry, pojawianie się nowych wykwitów skórnych lub powiększenie wcześniej istniejących zmian w ciągu ostatniego miesiąca. Najnowsza klasyfikacja wyróżnia pięć typów twardziny ograniczonej: ograniczona, uogólniona, linijna, głęboka i mieszana. Zaproponowano wiele metod oceny aktywności lub nasilenia choroby oraz uszkodzenia tkanek, takich jak ultrasonografia, termografia, durometria, tomografia komputerowa czy rezonans magnetyczny. Ograniczenia powyż-szych badań wynikają z możliwości oceny tylko jednego wykładnika -aktywności lub nasilenia choroby albo uszkodzenia tkanek. Przedstawiona metoda ewaluacji pacjentów oparta na zastosowaniu kwestionariusza do oceny aktywności i nasilenia choroby (LoSCAT) jest godna uwagi ze względu na dostępność narzędzia, powtarzalność wyników, a także czułość formularza na zmiany wynikające z zastosowanego leczenia.

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Section: Twardzina Linijnaunclassified

Section: Mixed Form Of Localized Sclerodermaunclassified

Section: Twardzina Linijnamentioning

confidence: 99%

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Localized scleroderma – classification and tools used for the evaluation of tissue damage and disease activity/severity

Wolska-Gawron¹,

Krasowska²

2017

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“…Clinically, it is characterized by a marked unilateral facial asymmetry; however, 5% and 10% of cases being bilateral have also been reported 8 . The asymmetry is preceded by a change in epidermal hue, by hyperpigmentation or depigmentation.…”

Section: Introductionmentioning

confidence: 99%

Parry-Romberg syndrome in a pediatric patient. A case report.

2015

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Abstract:The Parry-Romberg syndrome is a rare degenerative disease of unknown etiology that has dental implications. It is characterized by a progressive hemifacial atrophy that appears in the early stages of life. It causes aesthetic, functional and psychological alterations, and has social implications for the patient. There is no definitive treatment for the Parry-Romberg syndrome. Systemic and immune alterations produce oral and maxillofacial manifestations, which need to be managed by specialized dental professionals. The aim of this paper is to do a literature review of the Parry-Romberg syndrome and describe the oral and clinical characteristics of this condition in a 12-year-old male pediatric patient, who had a history of neurological disorders and facial asymmetry on the left side. Dentists require an adequate knowledge of the clinical and dental characteristics of this syndrome. With early diagnosis and appropriate surgical and orthodontic treatment at an early age, they can improve the quality of life of patients and minimize invasive long-term effects.

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Clinico-radiological approach to cerebral hemiatrophy

et al. 2018

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A systematic approach, linking both clinical and neuroimaging features, is important to facilitate the diagnostic workup of cerebral hemiatrophy. This may potentially help avoid large-scale investigations. Determining the underlying aetiology of cerebral hemiatrophy may impact treatment and prognostication as some conditions such as Rasmussen encephalitis and Parry-Romberg syndrome may benefit from timely implementation of immunomodulatory therapy.

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Parry Romberg Syndrome with localized scleroderma: a case report

Cited by 22 publications

References 13 publications

Localized scleroderma – classification and tools used for the evaluation of tissue damage and disease activity/severity

Localized scleroderma – classification and tools used for the evaluation of tissue damage and disease activity/severity

Parry-Romberg syndrome in a pediatric patient. A case report.

Clinico-radiological approach to cerebral hemiatrophy

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