Papillary-cystic neoplasm of the pancreas

Poustchi-Amin, Mehdi; Leonidas, John C.; Valderrama, Elsa; Shende, Ashok; Paley, Carole; Lanzkowsky, Philip; Kutin, Neil D.

doi:10.1007/bf02015781

Cited by 17 publications

(8 citation statements)

References 7 publications

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“…The typical tools used to diagnose SPT are abdominal US and CT scan. Solid pseudopapillary tumors appear as a solid, well-demarcated mass, usually heterogeneous in echo texture, sometimes containing hypoechoic fluid-filled cystic areas when viewe d by US [13][14][15]. Comput ed tom ography scans show a heterogeneous mass, often with peripheral contrast enhancement corresponding to the fibrous pseudocapsul e [15].…”

Section: Discussionmentioning

confidence: 96%

Solid pseudopapillary tumor of the pancreas: a multicenter study of 23 pediatric cases

Choi¹,

Kim²,

Oh³

et al. 2006

Journal of Pediatric Surgery

111

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Section: Discussionmentioning

confidence: 96%

Solid pseudopapillary tumor of the pancreas: a multicenter study of 23 pediatric cases

Choi¹,

Kim²,

Oh³

et al. 2006

Journal of Pediatric Surgery

111

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“…Unfortunately, preoperative laboratories and imaging are not specific for SPT. Ultrasound, CT and MRI reveal a well-demarcated mass ranging from mostly cystic to mostly solid 6 7 37. Imaging findings are detailed in box 1.…”

Section: Discussionmentioning

confidence: 99%

Solid pseudopapillary tumour (Frantz’s tumour) of the pancreas in childhood

Escobar

Bond²,

Schopp³

2014

BMJ Case Reports

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An 11-year-old girl presented with acute pancreatitis and mass in the head of the pancreas. MRI revealed a heterogeneous right-upper quadrant retroperitoneal mass measuring 6.8×6.1×5.5 cm arising from the pancreatic head. Endoscopic ultrasound with fine-needle aspirate revealed a solid pseudopapillary tumour (SPT) of the pancreas. The patient underwent a pylorus-preserving Whipple procedure. Pathology confirmed SPT. First described by Frantz, SPT represents less than 3% of all exocrine tumours. It is especially rare in children and shows different clinical features compared with adults. In our patient, tumour cells were arranged at the periphery of fibrovascular cores, but they did not show definite gland formation, keratinisation or cytoplasmic pigment accumulation. A periodic acid-Schiff stain without diastase did not show appreciable glycogen within the tumour cells, classic for Frantz's tumour. The literature, diagnosis, management and pathogenesis on this rare entity in children are reviewed and discussed.

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“…[1][2][3] Solid pseudopapillary neoplasm in children is rare. [4][5][6][7] Because of the rarity of this neoplasm, the reported information available is limited. To our knowledge, there is no prior report of a comparison of the clinical and pathological features in adults and children.…”

mentioning

confidence: 99%

Clinical Features and Outcome of Solid Pseudopapillary Neoplasm

Lee¹

2008

Arch Surg

140

101

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To delineate the clinical and pathological characteristics of solid pseudopapillary neoplasm (SPN), compare them between adults and children, and determine the predictive features suggesting malignant potential. Design: Retrospective analysis of patients who underwent surgery for a pathologically confirmed SPN. Setting: Tertiary care referral center. Patients: Sixty-two consecutive patients who underwent surgery for a pathologically confirmed SPN between 1985 and 2006. Main Outcome Measures: Demographic information and clinical presentation, radiological details, surgical data, pathological characteristics, postoperative course, and long-term survival. Results: Among 62 patients, 47 patients were adults (mean age, 36 years; range, 18-63 years) and 15 patients were children (mean age, 12 years; range, 8-13 years). A palpable mass was the most common presenting symptom in children (9 of 15; 60%) and an incidentally detected pancreatic mass, in adults (18 of 47; 38.3%) (P =.001). The mean tumor size in children was significantly larger than in adults (8.0 vs 6.0 cm; PϽ.03). In children, the tumor was located in the head of the pancreas (10 of 15; 66.7%) and in adults, in the body or tail (38 of 47; 80.9%) (P =.001). Nine patients (14.5%) had malignant SPN. There was no significant clinical factor suggesting malignant potential. Two patients had a tumor recurrence. They were still alive after debulking surgery. There were no tumor-related deaths. Conclusion: Solid pseudopapillary neoplasm had different clinical features in adults and children. Because long-term survival can be achieved, even with the synchronous or metachronous metastatic lesions, SPN should be treated aggressively, with complete resection, even if this requires metastatectomy.

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Papillary-cystic neoplasm of the pancreas

Cited by 17 publications

References 7 publications

Solid pseudopapillary tumor of the pancreas: a multicenter study of 23 pediatric cases

Solid pseudopapillary tumor of the pancreas: a multicenter study of 23 pediatric cases

Solid pseudopapillary tumour (Frantz’s tumour) of the pancreas in childhood

Clinical Features and Outcome of Solid Pseudopapillary Neoplasm

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