P25.04: Postnatal follow-up study of heterotaxy syndrome in a Korean population

Abstract

Poster abstracts nor functional cardiac anomalies were taken into account for this purpose. Results: A total of 57 (3.8%) cases of sCHD were found in the entire population, the incidence of sCHD was 3.25% in DC, 4.35% in MC and in TTTS cases was about 8%. 34 (59.6%) of cases underwent selective feticide because of either associated anomalies or severity of CHD. 7 (12.3%) died spontaneously in-utero and 16 were followed until birth, 75% of which was preterm (mean gestational age 29 +/− 2 weeks). 4 (25%) of cases were severe pulmonary stenosis (all of them in previous TTTS cases), two of which underwent pulmonary valvuloplasty at 4 th and 7 th day of life. 4 (25%) presented anomalous vein drainage systemic (3) and pulmonary (1). 3 (18.7%) fulfilled criteria for Fallot tetralogy. 3 (18.7%) had aortic coarctation. 2 (12.5%) presented cono-truncal anomalies (TGA and truncus). Neonatal intensive care stay was very long (mean of 74 +/− 23 days) because of prematurity and surgical interventions. Conclusions: sCHD have a higher incidence among twins, in TTTS the incidence of pulmonary stenosis is even higher than in other twins. Cardiac thorough screening is mandatory in all TP, particularly in MC. P25.07The clinical presentation and outcome of fetal isolated ductus arteriosus aneurysms