Here, we present a very rare entity of IEN-type IgA pemphigus with in addition circulating LAD antibodies concomitant with an exacerbation of ulcerative colitis. The coexistence of autoimmune bullous disorders and ulcerative colitis has been previously reported, 2 including epidermolysis bullosa acquisita, 3 linear IgA disease 4 and rarely IgA pemphigus. 5 There is only