Appendiceal primary peritoneal surface malignancies are rare and include a broad spectrum of pathologies ranging from indolent disease to aggressive disease. As such, the data that drive the management of appendiceal peritoneal surface malignancies is generally not based on prospective clinical trial data, but rather consists of level 1 data based on retrospective studies and high-volume institutional experiences. Complete surgical debulking typically offers the best chance for long-term survival. This review highlights the landmark articles on which management of primary appendiceal peritoneal surface malignancies are based.Appendiceal neoplasms are rare and involve a spectrum of diseases that can be either low grade with fairly slow growth rates or high grade with aggressive features. Broadly, appendiceal neoplasms account for only 1-2 % of intestinal malignancies. 1,2 Appendiceal malignancies may present with acute appendicitis, or more frequently, with progressive abdominal discomfort. Patients with appendiceal cancers may also be asymptomatic, and diagnosed secondary to identification of an abnormality noted on cross-sectional imaging, at the time of colonoscopy with an abnormal-appearing appendiceal orifice or at the time of surgery for another indication.