“…OPK has occasionally been reported in association with dermatofibrosis lenticularis disseminata, a predisposition to keloid formation, scleroderma-like lesion, plantar and palmar keratomas, rheumatoid arthritis, lupus erythematosus, ankylosing spondylitis, familial Mediterranean fever, synovial chondromatosis, exostoses, melorheostosis, osteitis condensans, Klippel-Feil syndrome, chondrosarcoma, osteosarcoma, giant cell tumor, dwarfism, dystocia, premyelopathic syndrome due to spinal stenosis, coarctation of aorta, double ureter, dacryocystitis, endocrine dysfunction, and dental and facial abnormalities. Association with connective tissue nevi called dermatofibrosis lenticularis disseminata (DLD) was found in nearly 25% of cases and overlapping of OPK and DLD was defined as Buschke-Ollendorff syndrome [ 4 – 6 , 9 ].…”