Ocular Advancement in Monobloc Distraction

Abstract

Forward movement of the globe following monobloc distraction has not previously been described. Although there is no current evidence for optic nerve stretch and compromise in monobloc surgery, the functional implications of these findings should be formally assessed.

Guideline for Care of Patients With the Diagnoses of Craniosynostosis

“…Kamoshima 149 describes the results of this intervention in 3 children as follows: “excellent functional and cosmetic outcome, with no remarkable complication.” Fitzgerald O’Conner described 10 syndromic craniosynostosis patients who underwent monobloc distraction. 150 The CT scans (pre- and postsurgery) demonstrated adequate advancement of the bony orbits, including forward advancement of the eyeball.…”

A case of Pfeiffer syndrome with c833_834GC>TG (Cys278Leu) mutation in theFGFR2gene

“…The prognosis of Pfeiffer syndrome depends on accompanying anomalies, and multiple surgeries are needed to release the prematurely closed sutures19, 20). In conclusion, this report describes a case of Pfeiffer syndrome with a novel c833_834GC>TG mutation (encoding Cys278Leu) in the FGFR2 gene, with an everted coccyx resembling a tail and increased ALP activity.…”

Avaliação do volume orbitário nos avanços frontofaciais

“…Still, there was no statistically significant difference between the postoperative orbital volumes when compared to normal ranges. 5,8,9,11,12,[14][15][16][17][18][19][20][21][22] .…”

“…O alongamento ósseo gradual tem sido utilizado com êxito na correção das deformidades craniofaciais (congênitas ou adquiridas), permitindo tanto o alongamento dos tecidos ósseos e moles. Atualmente, é considerado o tratamento de eleição nos pacientes portadores de craniofaciossinostoses sindrômica 6,8,9,14,[16][17][18][19][20][23][24][25][26][27][28][29][30][31][32][33][34][35][36][37][38] . A utilização desta técnica cirúrgica tem se propagado, sendo amplamente utilizada nos centros de referências mundiais.…”

“…Inúmeros trabalhos vêm sendo descritos na literatura mundial, que nos servem de parâmetros para estudos comparativos, sendo comum os autores publicarem suas experiências com o alongamento ósseo gradual em osteotomias para avanço do terço médio da face em grupos isolados de pacientes Le Fort III (LF III) 16,28,29,32,33,36 ou Monobloco (MB) 12,17,18,20,22 .…”