Multilocular cystic nephroma: A case report and review of the literature

Adult Multiloculated Cystic Nephroma: A Case Report

“…Radiologically, MCN usually presents as a solitary, centrally located, approximately 6-cm tumor consisting of small noncommunicating small cysts (6) . Ultrasonography is usually performed as s first-line diagnostic tool and commonly seen in contrast -enhanced CT as a unilateral mass with irregular cysts containinng watery fluid and septae of variable thickness (7) . Sometimes, extension into the renal pelvis may be seen, which results in hydronephrosis and hemorrhage and usually resembled as category III Bosniak classification (8)(9) .…”

“…Nephron-sparing surgery is the suggested surgical treatment modality for a small renal mass. Even though surgery remains the standard of care for small renal tumors, cryoablation and radiofrequency ablation have emerged as minimally invasive treatment alternatives (7)(8)(9)(10)(11)(12)13) . In our case, due to tumor size, similarity to cystic renal cell carcinoma and renal hydatid cyst, we decided to perform open total nephrectomy.…”

Multilocular Cystic Nephroma—A Brief Review

“…Bahubeshi et al reported that mutation of germline DICER1 is associated with familial cystic nephroma [4].…”

“…It's usually a mixed mesenchymal and epithelial [1] [2] [3], slow growing, unilateral mass of the lower pole of the kidney composed of numerous cysts, without solid elements. It has an excellent prognosis [4]. While the clinical, radiologic, and histologic features of cystic nephroma are well described, the immunohistochemical features are not [5].…”

Multicystic nephroma: a rare benign renal tumor with diagnostic predicament

“…6 Some genetic studies hypothesise that DICER1 mutation and hotspot missense mutation to be associated with MCN. 2,10 Although surgery remains the best treatment option, due to its benign nature partial nephrectomy or nephron sparing surgery can be done depending on the location and size of the MCN. 4…”