Megalourethra with posterior urethral valves

Abstract

A case of scaphoid megalourethra associated with the posterior urethral valves was seen in a 4-year-old male. The embryology of the anomaly and its management are discussed with a review of the literature.

Posterior urethral valve associated with orthotopic ureterocele

“…Statistically, cryptorchidism forms the most common associated congenital anomaly with posterior urethral valves; Kruger et al , in a review of 207 male children with posterior urethral valves discerned an overall incidence of cryptorchidism of 12 per cent. [1] Unicaliceal kidney, partial urethral duplication, and scaphoid megalourethra have been described as rare associated congenital anomalies with posterior urethral valves[2–4]…”

Congenital scaphoid megalourethra associated with posterior urethral valve: A case report

“…Patients present with ballooning of the glanular part of the penis and straining during micturition. In addition, this congenital pathology may be accompanied by other congenital urological anomalies [1][2][3]. We describe a rare combination of the case of a one and half year old male patient presenting with these complaints and discuss its treatment.…”

“…Moreover, its association with posterior urethral valves is still rarer [2,3]. Patients present with ballooning of the glanular part of the penis and straining during micturition.…”

Concomitant Anterior and Posterior Urethral Valves: A Comprehensive Review of Literature

“…7,20-22 However, a different approach would be following the Occam's razor or diagnostic parsimony to explain the embryology of concomitant AUV/D and PUV. This approach may also provide some explanation for concurrent presence of PUV with megalourethra [23][24][25] and to a lesser extent concurrent presence of prune belly syndrome and anterior urethral anomalies. [26][27][28][29] Taking all these anomalies into consideration, the most reasonable explanations lie in the mesenchymal origin and an early obstructive insult.…”