Mayer-Rokitansky-Küster-Hauser Syndrome: Sexuality, Psychological Effects, and Quality of Life

Bean, E.J.; Mazur, Tom; Robinson, Adjoa

doi:10.1016/j.jpag.2008.11.006

Cited by 125 publications

(119 citation statements)

References 43 publications

(113 reference statements)

Supporting

Mentioning

102

Contrasting

Unclassified

Order By: Relevance

“…Timely counseling and psychological support, both at the time of diagnosis and during the subsequent gynecological management are recommended [5,[8][9][10][11][12]. This study confirms the severity of the initial psychological reaction of youths to the diagnosis of MRKHS and the need for intervention in order to prevent possible immediate and long-term psychological consequences and to achieve a satisfactory transition to adulthood.…”

Section: Discussionsupporting

confidence: 67%

“…These previous reports show that MRKHS patients' awareness of their anomaly may produce psychological problems and that youths with PCOS express dissatisfaction with their appearance, which has a negative effect on their self-esteem and self-confidence [5][6][7].…”

Section: Discussionmentioning

confidence: 89%

“…There may also be metabolic disturbances, with insulin resistance and obesity, hirsutism, acne and alopecia [4]. term outcome of the syndrome, have been documented [5,[8][9][10][11][12]. In the case of PCOS, the need for a holistic approach has been also emphasized [13][14][15][16].…”

Section: Introductionmentioning

confidence: 99%

See 2 more Smart Citations

Untitled

2015

JPCPY

View full text Add to dashboard Cite

Section: Discussionsupporting

confidence: 67%

Section: Discussionmentioning

confidence: 89%

See 1 more Smart Citation

Untitled

2015

JPCPY

View full text Add to dashboard Cite

“…21 Most of these patients have functioning ovaries, which would therefore allow for in-vitro procedures through the use of a female surrogate which remains to be explored in the future.…”

Section: Discussionmentioning

confidence: 99%

Surgical and functional outcome of sigmoid colon-vaginoplasty in Mayer-Rokitansky-Kuster-Hauser syndrome

Pan¹

2017

Int J Reprod Contracept Obstet Gynecol

View full text Add to dashboard Cite

Background: The objective of this study is to report our experience with sigmoid vaginoplasty in adolescent female patients of Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome with emphasis on the effectiveness of surgery, complications, sexual and functional outcomes.Methods: A retrospective study of adolescent females with vaginal atresia and Mayer-Rokitansky-Kuster-Hauser syndrome. The sigmoid segment was used for vaginoplasty in all the case.Results: Eleven females were studied over a period of 15 years. Postoperative complications were perineal rash in 3, ileus in 3, and minor wound infection in 1 patient and urinary tract infection in one patient. Nine patients were on regular follow-up. All the neovaginas were patent and functional. The postoperative mean vaginal length was 12.1 cm (range 11 cm to 14 cm). One of the patients had mild vaginal stenosis which responded to vaginal dilation, one had mucosal prolapse of the neovagina, one had excessive mucus discharge, during follow-up visits. Out of the 11patients, 8 patients are sexually active and 7 reported that they were engaging in satisfactory sexual activity with mild or no pain, and with good mucosal sensitivity. Only one experienced dyspareunia and three patients had not participated in sexual activity.Conclusions: Sigmoid vaginoplasty is a safe and acceptable procedure for vaginal agenesis with good cosmetic results and acceptable complications rate. Sigmoid colon vaginoplasty is the treatment of choice because of its large lumen, thick walls resistant to trauma, adequate secretion allowing lubrication, not demanding prolonged dilatation and short recovery time.

show abstract

“…As the surgical approach is chosen, uterine remnants can be removed to avoid future endometriosis (1) . Patients who want to have children should be encouraged to adopt, or the possibility of having biological children by means of assisted reproduction techniques should be suggested, considering that the presence of functional ovaries in these women allow the production of normal ovules (10) . Even with the recent developments in the management of this syndrome, its diagnosis causes significant psychological distress, affecting the patients' quality of life because of the absence of menstruation and impossibility of pregnancy.…”

Section: Introductionmentioning

confidence: 99%

Síndrome de Mayer-Rokitansky-Kuster-Hauser: relato de caso e revisão da literatura

et al. 2011

View full text Add to dashboard Cite

The authors describe the case of a young female patient with primary amenorrhea and normal secondary sexual characteristics. The diagnostic investigation demonstrated the occurrence of Mayer-Rokitansky-Kuster-Hauser's syndrome. Keywords: Paramesonephric (Müllerian) ducts; Abnormalities.Os autores descrevem o caso de uma paciente jovem com amenorreia primária e caracteres sexuais secundários normais. A investigação diagnóstica constatou a ocorrência da síndrome de Mayer-Rokitansky-Kuster-Hauser. Unitermos: Ductos paramesonéfricos; Anormalidades. AbstractResumo

show abstract

Mayer-Rokitansky-Küster-Hauser Syndrome: Sexuality, Psychological Effects, and Quality of Life

Cited by 125 publications

References 43 publications

Untitled

Untitled

Surgical and functional outcome of sigmoid colon-vaginoplasty in Mayer-Rokitansky-Kuster-Hauser syndrome

Síndrome de Mayer-Rokitansky-Kuster-Hauser: relato de caso e revisão da literatura

Contact Info

Product

Resources

About