2006
DOI: 10.1080/10428190500285285
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Lymphoma of mucosa-associated lymphoid tissue in common variable immunodeficiency

Abstract: Common variable immunodeficiency (CVID) is the most common symptomatic primary immunodeficiency characterized by reduced levels of all major immunoglobuline classes and recurrent c infections. The risk of non-Hodgkin's lymphoma (NHL) among patients with CVID was found to be increased in different studies. Mucosa-associated lymphoid tissue (MALT) lymphomas are a recently recognized sub-set of low-grade B-cell NHL composed of marginal zone-related cells. MALT lymphomas appear in the lymphoid tissues as a result … Show more

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Cited by 58 publications
(27 citation statements)
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“…Le lymphome MALT se développe à partir des lymphocytes du tube digestif, surtout quand ils sont soumis à une stimulation inflammatoire ou auto-immune chronique [3,4]. Pour cette raison, plusieurs endoscopies de dépistage ont été effectuées à partir de 2001.…”
Section: Discussionunclassified
“…Le lymphome MALT se développe à partir des lymphocytes du tube digestif, surtout quand ils sont soumis à une stimulation inflammatoire ou auto-immune chronique [3,4]. Pour cette raison, plusieurs endoscopies de dépistage ont été effectuées à partir de 2001.…”
Section: Discussionunclassified
“…21 MZL almost exclusively affects adults, although rare cases in younger patients have been reported. 17,22 Patients with MZL may present with cough, fever, or unexplained weight loss, although many are entirely asymptomatic. The most common radiologic findings are presence of solitary or multiple discrete nodules or areas of consolidation that may occupy one or both lungs in either perihilar or peripheral distribution.…”
Section: Lymphomas (Non-hodgkin) Of B-cell Lineage Primary Pulmonary mentioning
confidence: 99%
“…Le déficit immunitaire induit par la lymphangiectasie intestinale semble, comme les autres déficits immunitaires, favoriser les lymphomes digestifs qui surviennent assez tardivement [2] . Le lymphome MALT se développe à partir des lymphocytes du tube digestif, surtout quand ils sont soumis à une stimulation inflammatoire ou auto-immune chronique [3,4] . [5] .…”
unclassified