“…This is thought to refiect an underlying mosaicism or chimerism, and several cytogenetic alterations have been described. Occasionally, it is associated with systemic abnormalities, including developtnental and growth retardation, facial and body asymmetry, and cardiac defects (2,3). Histology shows hyperpigmentation of the basal epidermal layer and prominent melanocytes, without pigment incontinence.…”