Lethal Pulmonary Hypoplasia and Hydrocolpos With Transverse Vaginal Septum in a Newborn: A Case Report and Review of the Literature

The presence of distal atretic vagina causing accumulation of fluid and mucus secretions in the proximal vaginal cavity resulted in fetal hydrocolpos. Obstructive uropathy developed gradually because of direct compression of hydrocolpos on bilateral lower ureters, resulting in oligohydramnios from decreased urine formation. Oligohydramnios inhibited normal mandibular development with resulting cleft palate and glossoptosis (Pierre Robin Sequence). The development of sequence of events in this case indicates Pierre Robin Sequence as another effect of Oligohydramnios Sequence arising out of deformational forces acting on cranio-facial structures.

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Lethal Pulmonary Hypoplasia and Hydrocolpos With Transverse Vaginal Septum in a Newborn: A Case Report and Review of the Literature

Abstract: This is a case report of an unusual cause of Potter sequence. Autopsy showed lethal pulmonary hypoplasia in association with a transverse vaginal septum, hydrocolpos, and a secondary obstructive uropathy.

Cited by 4 publications

References 48 publications

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“Z”-plasty of the transverse vaginal septum using Garcia’s procedure and the Grünberger modification

Fetal Hydrocolpos Leading to Pierre Robin Sequence: An Unreported Effect of Oligohydramnios Sequence

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