“…It is characterized by presence of three atria in the heart, due to a fibro-muscular membrane giving rise to an accessory chamber in the left atrium, most cases are found after autopsy (0.4 %). It is usually associated with ASD and total anomalous pulmonary drainage to the right atrium, bicuspid aortic valve, tetralogy of Fallot and double outlet right ventricle [4] , [5] , [6] .…”