Insight into congenital absence of the portal vein: Is it rare?

Shen, Guohua; Zhu, Jin Yang‚ Jin-Hua Mei‚ Yue-Feng

doi:10.3748/wjg.14.5969

Cited by 76 publications

(46 citation statements)

References 117 publications

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“…[89] At 5 weeks gestational age, the right and left vitelline veins forms a branching venous plexus around the duodenum, comprising two components ventral to the duodenum and one component dorsal to the duodenum, before terminating in the sinus venous. By 10 weeks, selective involution of portions of this venous plexus gives rise to the adult portal vein.…”

Section: Discussionmentioning

confidence: 99%

Anatomic Variations of the Right Portal Vein: Prevalence, Imaging Features, and Implications for Successful Transjugular Intrahepatic Portosystemic Shunt Creation

Gunasekaran

Gaba

2017

Journal of Clinical Imaging Science

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Given the widespread use of transjugular intrahepatic portosystemic shunt (TIPS) creation for the treatment of portal hypertensive complications, a working knowledge of portal venous anatomy is critical for interventional radiologists. The right portal vein – which is most commonly accessed during TIPS – is subject to various anatomic variants that may potentially impact procedure success. This pictorial essay characterizes the anatomic patterns of the right portal vein branching in terms of type and frequency based on case series review. The work also explains the potential procedural implications of the right portal vein anatomic variations as they pertain to TIPS technical success.

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Section: Discussionmentioning

confidence: 99%

Anatomic Variations of the Right Portal Vein: Prevalence, Imaging Features, and Implications for Successful Transjugular Intrahepatic Portosystemic Shunt Creation

Gunasekaran

Gaba

2017

Journal of Clinical Imaging Science

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“…Both males had a single b-HCA transformed in HCC and the female had multiple H-HCA. Focal liver cell lesions including HCA, HCC, focal nodular hyperplasia, and nodular regenerative hyperplasia have been reported in association with congenital absence of the portal vein, also known as congenital extrahepatic portosystemic shunt or Abernethy malformation [5–8, 25–27]. It has been suggested that the decreased venous blood flow combined with an increased arterial blood flow could result in abnormal perfusion of the liver and to uneven vascular perfusion of the liver giving rise to a hyperplastic response, and to a spectrum of nodular lesion including HCA [5, 28].…”

Section: Discussionmentioning

confidence: 99%

Histological and Immunohistochemical Revision of Hepatocellular Adenomas: A Learning Experience

Fonseca

Hoton

Dardenne

et al. 2013

International Journal of Hepatology

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Light has been shed on the genotype/phenotype correlation in hepatocellular adenoma (HCA) recognizing HNF1α-inactivated HCA (H-HCA), inflammatory HCA (IHCA), and β-catenin-activated HCA (b-HCA). We reviewed retrospectively our surgical HCA series to learn how to recognize the different subtypes histopathologically and how to interpret adequately their immunohistochemical staining. From January 1992 to January 2012, 37 patients underwent surgical resection for HCA in our institution. Nine had H-HCA (25%) characterized by steatosis and loss of L-FABP expression; 20 had IHCA (55.5%) showing CRP and/or SAA expression, sinusoidal dilatation, and variable inflammation; and 1 patient had both H-HCA and IHCA. In 5 patients (14%), b-HCA with GS and β-catenin nuclear positivity was diagnosed, two already with hepatocellular carcinoma. Two cases (5.5%) remained unclassified. One of the b-HCA showed also the H-HCA histological and immunohistochemical characteristics suggesting a subgroup of β-catenin-activated/HNF1α-inactivated HCA, another b-HCA exhibited the IHCA histological and immunohistochemical characteristics suggesting a subgroup of β-catenin-activated/inflammatory HCA. Interestingly, three patients had underlying vascular abnormalities. Using the recently published criteria enabled us to classify histopathologically our retrospective HCA surgical series with accurate recognition of b-HCA for which we confirm the higher risk of malignant transformation. We also underlined the association between HCA and vascular abnormalities.

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“…The number of cases of Abernethy syndrome has increased in recent years, due to advances in imaging techniques 2.…”

Section: Introductionmentioning

confidence: 99%

Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome

Christou

Dib

Chuffart

et al. 2018

Clinical Case Reports

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Insight into congenital absence of the portal vein: Is it rare?

Abstract: Congenital

Cited by 76 publications

References 117 publications

Anatomic Variations of the Right Portal Vein: Prevalence, Imaging Features, and Implications for Successful Transjugular Intrahepatic Portosystemic Shunt Creation

Anatomic Variations of the Right Portal Vein: Prevalence, Imaging Features, and Implications for Successful Transjugular Intrahepatic Portosystemic Shunt Creation

Histological and Immunohistochemical Revision of Hepatocellular Adenomas: A Learning Experience

Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome

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