IgG4-related Lung Disease

Raj, Rishi; Boddipalli, Viveka; Brown, C. M.; Dematte, Jane; Raparia, Kirtee

doi:10.1097/cpm.0000000000000057

Cited by 3 publications

(3 citation statements)

References 59 publications

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“…IgG4-RLD occurs in 12–50% of patients with IgG4-RD [3], [4], [5]. Mediastinal adenopathy is most common and pulmonary involvement takes the form of pulmonary nodules or masses [3], [6], [7], [8]. As shown in Fig.…”

Section: Discussionmentioning

confidence: 98%

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A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease

Touge

Tomita

Yamasaki

et al. 2017

Respiratory Medicine Case Reports

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IgG4-related lung disease (IgG4-RLD) is a rare and chronic progressive autoimmune disease. We report a case of IgG4-related inflammatory pseudo-tumor of the lung that was seropositive for proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA). A 61-year-old male had a mass lesion in the right lower lung field in chest X-ray. Transbronchial lung biopsy resulted in a pathological diagnosis of IgG4-RLD. The condition was improved by hormonal therapy.

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Section: Discussionmentioning

confidence: 98%

“…IgG4-related lung disease (IgG4-RLD) has been described as interstitial pneumonia and inflammatory pseudo-tumor [2], [3], [4], [5], [6], [7]. Proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) is well known as a disease marker in Wegener's granulomatosis [8].…”

Section: Introductionmentioning

confidence: 99%

A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease

Touge

Tomita

Yamasaki

et al. 2017

Respiratory Medicine Case Reports

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show abstract

“…It can be seen in 5% of normal people, or in 10% patients with malignant tumors of the biliopancreatic system or other infectious diseases and inflammatory diseases [85]. The sensitivity and specificity of the diagnosis of IgG4-RD through serum lgG4 level were 63% and 94% respectively [86,87]. 3-30% of patients had normal serum IgG4 level [88].…”

Section: Discussionmentioning

confidence: 99%

IgG4-related lung disease: A case report and literature review

Ren¹,

Han²,

Wang³

2022

J Clin Images Med Case Rep

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A case of immunoglobulin G4-related lung disease with bilateral diffuse infiltration

Liu

Zhang²,

Liu³

et al. 2017

Medicine

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Rationale:Immunoglobulin (Ig) G4-related disease (IgG4-RD) is a rare and chronic progressive autoimmune disease. It is a novel clinical entity characterized by elevated serum IgG4 concentration and tissue infiltration by IgG4+ plasma cells. IgG4-related lung disease (IgG4-RLD) has been described as interstitial pneumonia and inflammatory pseudotumor, with various abnormal radiographic patterns. We report a case of IgG4-related lung disease with bilateral diffuse infiltration.Patient concerns:A 65-year-old woman was admitted to our hospital because of cough, sputum, and fever. Chest computed tomography (CT) revealed multifocal areas of consolidations, nodules, and ground glass opacities in both lungs. She still had fever after anti-infective therapy.Diagnoses:Bronchial bronchoscopy and percutaneous lung biopsy were performed, resulted in a pathological diagnosis of IgG4-RLD.Interventions:The patient was started on oral prednisolone 30 mg/day for 28 days, and then was gradually tapered.Outcomes:After one week treatment, the temperature was stable, CT showed significant improvement in the areas of consolidations and nodules.Lessons:It is a typical case of IgG4-RLD. This case indicated that suggestive evidence, radiological appearances, serum tests, pathological characteristics, and classic therapy IgG4-RLD. It is a rare disease that needs our more attention in future.

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IgG4-related Lung Disease

Cited by 3 publications

References 59 publications

A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease

A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease

IgG4-related lung disease: A case report and literature review

A case of immunoglobulin G4-related lung disease with bilateral diffuse infiltration

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