Idiopathic right atrial enlargement

Ostovan, Mohammad Ali; Shahrzad, Shahab; Taban, Samira; Moniri, Alireza

doi:10.1177/0218492312463148

Cited by 5 publications

(4 citation statements)

References 2 publications

(2 reference statements)

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“…The size of the dilated RA varied considerably. The largest RA (sized 19.5 × 15.2 cm) was found in a 26-year-old patient by Ostovan et al [27].…”

Section: Resultsmentioning

confidence: 99%

Clinical Presentation, Diagnosis, and Management of Idiopathic Enlargement of the Right Atrium: An Analysis Based on Systematic Review of 153 Reported Cases

Zhang

et al. 2020

Cardiology

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Idiopathic enlargement of the right atrium (IERA) is a rare cardiac anomaly, and only sporadic cases have been reported. Little is known about its clinical relevance, and inconsistencies in medical and surgical management remain among different settings. In this paper, we systematically reviewed the published cases of the IERA in terms of clinical presentation, diagnosis, and management. A total of 153 cases of IERA were covered. Arrhythmia, dyspnea, and palpitation were found to be the most common clinical manifestations. It tends to be associated with life-threatening complications and sudden cardiac death. Diagnosis was mostly established by using echocardiography. Presenting symptoms, abnormal ECG findings, and therapeutic modalities were significantly related to the prognosis of IERA. Symptomatic patients were significantly more likely to have poor outcomes than asymptomatic patients (<i>p</i> = 0.044), and conservative treatment was more associated with adverse outcomes compared to surgical resection (<i>p</i> = 0.016). In conclusion, IERA, although rare, tends to be associated with potential life-threatening complications and sudden cardiac death. Echocardiography is the most common diagnostic modality. Surgical resection is indicated for symptomatic patients.

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“…The size of the dilated RA varied considerably. The largest RA (sized 19.5 × 15.2 cm) was found in a 26-year-old patient by Ostovan et al [27].…”

Section: Resultsmentioning

confidence: 99%

Clinical Presentation, Diagnosis, and Management of Idiopathic Enlargement of the Right Atrium: An Analysis Based on Systematic Review of 153 Reported Cases

Zhang

et al. 2020

Cardiology

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“…The isolated malformations of the right atrium reported in the literature are very rare cardiac abnormalities, including the following morphological types of disease: diffusely enlarged right atrium (idiopathic enlargement or dilation of the right atrium), single or multiple saccular diverticula of the right atrium, giant right atrial aneurysm (GRAA), right atrial diverticulum (DERA), and aneurysms arising from a part of the right atrium or the coronary sinus [ 1 – 3 ]. The diagnosis of IERA and other right atrial malformations rely on a disproportionately enlarged right atrium compared to the other cardiac chambers in the absence of other cardiac abnormalities.…”

Section: Discussionmentioning

confidence: 99%

Surgical Treatment of Idiopathic Enlargement of the Right Atrium

Surace

Iezzi

Colaneri

et al. 2018

Case Reports in Surgery

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Idiopathic enlargement of the right atrium (IERA) is a very rare abnormality. Approximately one-half (48%) of the patients with a congenital enlargement of the right atrium have no symptoms. When they occur, symptoms include shortness of breath (28% of cases), palpitations (17%), arrhythmias (12%), and in rare cases, right heart failure and extreme tiredness. We report one such case of a young man with a disproportionally enlarged right atrium. The basal transthoracic echocardiogram demonstrated a huge right atrium with a thick smoke pattern and mild tricuspid regurgitation in the absence of congenital heart disease. Magnetic resonance imaging confirmed the right atriomegaly, with initial compression of the right ventricle, and excluded congenital heart defects or absence of pericardium. The patient underwent surgical resection of the right atrial wall and the atriotomy was closed, leaving an atrial chamber of normal consistency and size. The resected atrium had normal and homogeneous wall thickness without significant fibrosis which confirmed the diagnosis of an idiopathic enlargement of the right atrium.

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“…It has been defined as an increase in the right atrial long axis indexed to body surface area (men >2.6 cm/m 2 , women >2.8 cm/m 2 ) in the absence of other cardiac abnormalities 1. It can be congenital or acquired.…”

Section: Discussionmentioning

confidence: 99%

Idiopathic aneurysmal giant right atrial enlargement with thrombus formation

et al. 2014

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A 12-year-old boy presented to our outpatient department with progressive dyspnoea and palpitations of 6-month duration. Cardiovascular system examination revealed a short ejection systolic murmur at the left lateral heart border. Chest X-ray showed gross cardiomegaly. Two-dimensional ECHO revealed massive aneurysmal right atrial (RA) enlargement, low-pressure tricuspid regurgitation and dysplastic tricuspid valve with compression of the left atrium (LA) and left ventricle (LV). Cardiac CT showed grossly enlarged RA compressing the LA, LV, right pulmonary artery and right upper lobe pulmonary vein. Initially, the patient refused surgery. On follow-up, a thrombus was seen in the giant RA and the patient agreed to and underwent successful surgery. Absence of pericardium was specifically excluded on cardiac MRI and on surgery. Resected atrial tissue showed wall thinning and focal fibrosis establishing idiopathic dilation of the RA. The patient is on regular follow-up.

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Idiopathic right atrial enlargement

Cited by 5 publications

References 2 publications

Clinical Presentation, Diagnosis, and Management of Idiopathic Enlargement of the Right Atrium: An Analysis Based on Systematic Review of 153 Reported Cases

Clinical Presentation, Diagnosis, and Management of Idiopathic Enlargement of the Right Atrium: An Analysis Based on Systematic Review of 153 Reported Cases

Surgical Treatment of Idiopathic Enlargement of the Right Atrium

Idiopathic aneurysmal giant right atrial enlargement with thrombus formation

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