Ictiosis arlequín

Jiménez, M.J. Olmos; Fernandez, A. G.; Valverde-Molina, J.; Lorenzo, Marlén Pérez

doi:10.1016/j.anpedi.2013.06.019

Cited by 2 publications

(3 citation statements)

References 2 publications

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“…El manejo inicial de estos pacientes incluye extremar la higiene, calor húmedo en incubadora, alto aporte de líquidos para evitar deshidratación por las pérdidas transepidérmicas y pomadas emulsificantes [7].…”

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Silvia Zepeda Olivera

Olivera¹,

Santamaría²,

García³

et al. 2021

Rev. chil. anest.

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Introduction: Ichthyosis are hereditary disorders of keratinization which are characterized for the presence of hyperkeratosis and/or peeling. This disorder group can put in danger the life of the patient because of the severe alteration of the skin barrier, associated with a severe transdermic loss of water, different grades of hypothermia and a hypernatremic dehydration. Objective: Introducing the clinic case of an infant patient with the diagnosis of ichthyosis plus severe dehydration who is scheduled for placement of CVC. Clinical case: Male infant, 3 months old, with the diagnosis of ichthyosis and severe dehydration, scheduled for placement of CVC. Conclusions: Due to the urgency of our patient, who presented severe dehydration, an inhaled general anesthesia with sevoflurane and oxygen was decided, without instrumenting the airway which in these patients has the risk of being potentially difficult, from the placement of the face mask itself, until finding lesions within the oral cavity, ventilatory assistance should be maintained by the pediatric anesthesiologist, once venous access is achieved, the fluids restitution is performed with loads of 10 to 20 ml/kg of the patient's weight, hyperthermia was controlled with physical means.

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Silvia Zepeda Olivera

Olivera¹,

Santamaría²,

García³

et al. 2021

Rev. chil. anest.

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“…Skin manifestations often worsen in cold or dry environments. They usually present at birth with severe erythroderma, slight desquamation and bulla or large erosions that are distributed mainly in the trunk and limbs, which evolve to extensive denuded, moist, painful and ill smelling areas [5].…”

Section: Introductionmentioning

confidence: 99%

“…In turn, it may present with acquired disorders. They are distinguished by their mode of inheritance, clinical characteristics, associated defects and histological findings [1][2][3][4][5][6]. Several classifications of this pathology are known, Traupe proposed to divide them into vulgar, when the clinic is incipient at birth and congenital when they are marked at the time of birth [2].…”

Section: Introductionmentioning

confidence: 99%

Collodion Baby: Case Report

Fern¹,

Morazán²

2017

J Healthc Commun

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Ichthyosis is an infrequent clinical entity worldwide (1:300,000 births) that produces visible scales on all or a great part of the skin surface. The new classification of this weird dermatosis is divided into 36 groups and their subgroups depend on their frequency, heritage and extracutaneus manifestations. Among the autosomal recessive congenital ichthyosis, we can identify collodion baby, which describes a newborn, preterm most of the time, with a hard, tense, brilliant membrane covering the whole body. In this article we talk about the case of a collodion baby, preterm female newborn of 35 gestational weeks, attended at Hospital General del Sur, Choluteca, Honduras, whose mother had poor prenatal control, not performed by a physician, without obstetric ultrasound during pregnancy. At physical examination the new-born had a constrictive, tense membrane, similar to an oily parchment or collodion that covered the entire body surface, she was given the initial optimum management, but due to lack of service in the area of pediatric dermatology, neonatology and genetics, the decision to transfer the newborn to a hospital with a higher level of care was made. In Honduras this case would be the second reported in the country and the first in the southern region of the country.

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Ictiosis arlequín

Cited by 2 publications

References 2 publications

Silvia Zepeda Olivera

Silvia Zepeda Olivera

Collodion Baby: Case Report

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