“…The mucosal lesions in Darier's disease are uncommon and their incidence varies in different studies, ranging from 15% to 50% 3,4,10,12 . Most of the studies that have evaluated the mucosal involvement in Darier's disease concentrated on oral mucosa lesions, however, rectal mucosal involvement, 15 localized disease to the vulva, 16,17 salivary glands obstruction, 18 and hypopharyngeal and laryngeal involvement 19 have been reported.…”