Hemangiopericytoma in children

Congenital Hemangiopericytoma: Report of a Case

“…Reprint requests to: Y. Hamada (Received for publication on Feb. 12, 1999; accepted on Nov. 11,1999) appearance was consistent with a diagnosis of CHP. The patient has shown normal leg function and remains well with no recurrence for 7 years postoperatively.…”

“…10 In contrast, CHP is extremely rare, comprising only 3.3%-7.0% of all HPs. 11 In a large series of pediatric neoplasms, only 2.6% were congenital, and 3.0% of these were HPs. 2 A diagnosis of HP may be difficult.…”

Infantile Hemangiopericytoma: Two Cases Report and Literature Review

“…Infantile hemangiopericytoma is a rare vascular tumour in children below one year of age [4]. In 1942, Stout and Murray [5] first described hemangiopericytoma in the lungs as that arising from the vascular pericytes of Zimmermann which are contractile cells that spiral around capillary walls and differing from a glomus tumour or a hemangioma but they did not differentiate between infantile and adult forms.…”

“…Other authors have reported that radiotherapy is ineffective [14,15,23]. Metastatic disease has only been reported in three cases of congenital hemangiopericytoma [4,15,24] although the adult form of the tumour has a rate of distant metastasis of up to 56%, mainly to the lung and skeleton [8,25]. Careful follow up is therefore required.…”

Infantile Hemangiopericytoma

“…Characteristically, they are multilobulated, often with distinct in› travascular and perivascular satellite nodules outside the main tumour mass. Majority of the lesions are solitary [3] but multiple le› sions have been described [4,5]. Tumours are most common in the lower extremity espe› cially the thigh, the pelvic fossa and the retroperitoneum.…”