Hearing Loss and Enlarged Internal Auditory Canal in Children

Santos, Saturnino; Domínguez, M. J.; Cervera, J.; Suárez, Alicia; Bueno, Antonio; Bartolomé, Margarita; López, Rafael

doi:10.1016/j.otoeng.2013.11.014

Cited by 3 publications

(4 citation statements)

References 33 publications

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“…The relationship detected in this investigation may have been carried by a small number of outliers and needs to be followed up by further research. Bulbous IAC is a radiographic finding described in previous studies, and case series of children with SNHL and abnormal widening of the IAC have been described . However, an association between the enlarged BCNC and SNHL has yet to be established.…”

Section: Discussionmentioning

confidence: 99%

Bony cochlear nerve canal stenosis and speech discrimination in pediatric unilateral hearing loss

et al. 2015

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Section: Discussionmentioning

confidence: 99%

Bony cochlear nerve canal stenosis and speech discrimination in pediatric unilateral hearing loss

et al. 2015

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“…The relationship between dilated IAC and audiological findings is not clear. Studies demonstrate that dilated IAC is associated with sensorineural hearing loss [8][9][10]. However, most have inner ear malformations accompanying dilated IAC.…”

Section: Discussionmentioning

confidence: 99%

Identification of the audiological and temporal bone radiology manifestations of SOFT syndrome: a case report

Satici

Kartal

Topcuoğlu

et al. 2023

Egypt J Otolaryngol

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Background SOFT syndrome is characterized by prenatal onset growth retardation, brachydactyly, onychodysplasia, postpubertal onset hypotrichosis, normal psychomotor development, and facial dysmorphism including dolichocephaly, elongated triangular face, prominent forehead and nose, and abnormal ear structure. This syndrome has been described in 31 patients worldwide. Case presentation In this case report, the audiological and temporal bone radiological results of a 4-year- and 5-month-old patient with SOFT syndrome are presented. Bilateral internal acoustic canals (IAC) are dilated with lobulated contour. Conclusions This case report is the first in the literature as it reports audiological and temporal bone radiology observations in SOFT syndrome. It is thought that regular and detailed audiological and temporal bone radiology evaluations performed in patients with different SOFT syndrome will be a reference for determining the characteristic audiological and temporal bone radiological findings related to this syndrome.

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“…The prevalence of congenital sensorineural hearing loss (SNHL) is approximately 1-6 per 1,000 live births [3,4]. Hypoplasia of the IAC is a rare malformation, believed to be due to agenesis of the vestibulocochlear nerve (VCN) [5].…”

Section: Etiology and Demographicsmentioning

confidence: 99%

“…According to Wu C. et al, it is rare to find an anomalous course of FN in patients without abnormalities in the external ear or tympanic membrane, as presented in the case [11]. The diagnosis of IAC malformations with or without variances in the FN and bilateral VCN agenesis are usually made by MRI [3,4]. Moreover, computed tomography (CT) of the temporal bone can also evaluate this anatomic region [9,12].…”

Section: Clinical and Imaging Findingsmentioning

confidence: 99%

Internal auditory canal hypoplasia associated with bilateral vestibulocochlear nerve aplasia and deviant facial nerve course: A case report and MRI findings

et al. 2021

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The evaluation of internal auditory canals and cochlea has gained significant importance due to the increasing number of cochlear implantations worldwide. This region's anatomical study is essential for cochlear implant surgery using magnetic resonance imaging as the method of choice. We report a case of a 6-year-old male patient diagnosed with a rare bilateral malformation of the internal auditory canals associated with an aberrant course of the facial nerve and vestibulocochlear nerve aplasia. This report raises the importance of identifying this rare malformation for appropriate management and reinforces awareness of possible complications.

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Hearing Loss and Enlarged Internal Auditory Canal in Children

Cited by 3 publications

References 33 publications

Bony cochlear nerve canal stenosis and speech discrimination in pediatric unilateral hearing loss

Bony cochlear nerve canal stenosis and speech discrimination in pediatric unilateral hearing loss

Identification of the audiological and temporal bone radiology manifestations of SOFT syndrome: a case report

Internal auditory canal hypoplasia associated with bilateral vestibulocochlear nerve aplasia and deviant facial nerve course: A case report and MRI findings

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