Abstract:Question 1Is it necessary to distinguish between congenital medial capillary macula and lateral congenital capillary macula? Recommendation of good clinical practice, based on the experience of the panel: GGP grade. It is no supported by
EtiologyMost VM are sporadic. However, inherited forms with autosomal dominant inheritance have been reported.
“…It was the unique therapy proposed for years and now is often associated with embolization [ 4 , 18 ]. This combination is indicated when the AVM is small and appears to be focal and completely resectable; however, if the removal may not be completely performed, relapse could be present [ 16 ].…”
Section: Discussionmentioning
confidence: 99%
“…The lesion had a hard-elastic consistency, and it was nonpainful on superficial and deep palpation. According to the Guidelines for Vascular Anomalies draw up by the Italian Society for the study of Vascular Anomalies (SISAV) [ 16 ], the ultrasound was performed, in traditional technique, with 3D acquisition and, in multiple acquisition, with TUI (tomographic ultrasound imaging) technique. Color/power Doppler and 3D angio were performed to evaluate the vascularity.…”
Section: Methodsmentioning
confidence: 99%
“…Therefore, the aim of the present study was to describe a successful case of AVM of the tongue treated with rhodamine dye laser that was able to coagulate both capillaries and red vascular malformations, without involving the superficial epithelial layers, in order to avoid the invasiveness of the gold standard surgical excision or embolization [ 16 ].…”
Arteriovenous malformations (AVMs) are abnormal connections between blood vessels that bypass the normal capillary bed. To avoid the invasiveness of the gold standard surgical excision, the use of dye laser has been suggested as an alternative. A 53-year-old man in good overall health presented with a large bluish-red nodular growth covered by intact mucosa on the left side of his tongue. The growth had a hard-elastic consistency and was not painful to touch. Imaging investigations revealed a capsulated growth consistent with a diagnosis of AVM. The patient underwent two sessions of rhodamine dye laser treatment using the following parameters: fluence of 12 J/cm2, 6 mm laser spot, a single pulse with repetition up to 1.0 Hz, and a pulse duration of 3.0 ms. Follow-up examinations were conducted at 12, 24, 36, and 40 months after the treatment. At the 40-month follow-up, the lesion had reduced in size, with a more organized vascular network, and was not clinically detectable. Considering the limitations of this case report, the application of dye laser appears to be a potentially successful treatment option for AVMs.
“…It was the unique therapy proposed for years and now is often associated with embolization [ 4 , 18 ]. This combination is indicated when the AVM is small and appears to be focal and completely resectable; however, if the removal may not be completely performed, relapse could be present [ 16 ].…”
Section: Discussionmentioning
confidence: 99%
“…The lesion had a hard-elastic consistency, and it was nonpainful on superficial and deep palpation. According to the Guidelines for Vascular Anomalies draw up by the Italian Society for the study of Vascular Anomalies (SISAV) [ 16 ], the ultrasound was performed, in traditional technique, with 3D acquisition and, in multiple acquisition, with TUI (tomographic ultrasound imaging) technique. Color/power Doppler and 3D angio were performed to evaluate the vascularity.…”
Section: Methodsmentioning
confidence: 99%
“…Therefore, the aim of the present study was to describe a successful case of AVM of the tongue treated with rhodamine dye laser that was able to coagulate both capillaries and red vascular malformations, without involving the superficial epithelial layers, in order to avoid the invasiveness of the gold standard surgical excision or embolization [ 16 ].…”
Arteriovenous malformations (AVMs) are abnormal connections between blood vessels that bypass the normal capillary bed. To avoid the invasiveness of the gold standard surgical excision, the use of dye laser has been suggested as an alternative. A 53-year-old man in good overall health presented with a large bluish-red nodular growth covered by intact mucosa on the left side of his tongue. The growth had a hard-elastic consistency and was not painful to touch. Imaging investigations revealed a capsulated growth consistent with a diagnosis of AVM. The patient underwent two sessions of rhodamine dye laser treatment using the following parameters: fluence of 12 J/cm2, 6 mm laser spot, a single pulse with repetition up to 1.0 Hz, and a pulse duration of 3.0 ms. Follow-up examinations were conducted at 12, 24, 36, and 40 months after the treatment. At the 40-month follow-up, the lesion had reduced in size, with a more organized vascular network, and was not clinically detectable. Considering the limitations of this case report, the application of dye laser appears to be a potentially successful treatment option for AVMs.
“…For this reason, pediatric patients with suspected vascular abnormalities should be evaluated by an expert multidisciplinary team including clinicians, radiologists, surgeons, pathologists, and geneticists. The role of the reference Centre is crucial for (i) diagnosis, (ii) patient follow-up, (iii) to guide and accompany the patient and family during the chronic and frequently disabling disorder, and (iv) to participate to research in the field, and (v) to recruit patients in clinical trial for emerging targeted therapies ( 3 , 94 ).…”
Vascular anomalies of the pediatric orbit represent a heterogeneous group that include both vascular tumors and vascular malformations. The disorder may initially be silent and then associated with symptoms and/or function damage, depending on the type of vascular anomaly and its extension. Vascular tumors include benign, locally aggressive (or borderline) and malignant forms while vascular malformations are divided into “simple”, “combined” and syndromic, or “low flow” or “high flow”. Both entities can arise in isolation or as part of syndromes. In this review, we describe the imaging findings of the vascular lesions of the orbit in the pediatric population, which are key to obtain a correct diagnosis and to guide the appropriate treatment in the light of the new genetic and molecular discoveries, and the role of the radiologist in their multidisciplinary management. We will also touch upon the main syndromes associated with orbital vascular abnormalities.
“…Oral propranolol is the first line therapy for IHs during proliferative phase, having demonstrated efficacy, safety and tolerability ( 1 – 4 ). It is indicated for life-threatening, functional damaging and disfiguring infantile haemangiomas.…”
Infantile haemangiomas are very common benign tumours in the first months of life. They are mostly cutaneous; however, extracutaneous lesions are possible, and occur in very rare cases in the central nervous system. A European multicentre observational retrospective study was conducted in the last 5 years. Seven patients with intracranial or intraspinal infantile haemangiomas were selected and treated with oral propranolol. Propranolol was interrupted after complete or almost complete resolution of infantile haemangiomas. All patients tolerated the treatment well without side-effects. Central nervous system infantile haemangiomas are probably underestimated due to the frequent absence of symptoms and their spontaneous involution. However, they should be investigated in case of segmental cutaneous infantile haemangiomas, particularly on the head, neck, upper trunk, lumbar or sacral area in order to diagnose intra-central nervous system involvement at an early stage.
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