Glomangiosarcoma de novo in a child: A case report and review of literature

Malignant glomus tumors of the head and neck in children and adults: Evaluation and management

“…Median age of presentation with primary MGT was 47 years (interquartile range [IQR] = 30.5). Including our case, there were only two pediatric MGTs of the head and neck (cases 1 and 2) . Local invasion was reported in nine of 11 primary tumors and involved the trachea, larynx, esophagus, and carotid.…”

“…In the head and neck, local invasion can involve critical aerodigestive or neurovascular structures, making wide local excision problematic. In the case report of the 6‐year‐old child, carotid involvement was seen on MRI . They were able to achieve tumor resection without injury to the carotid, but the relationship to the carotid intraoperatively was not described.…”

“…Including our case, there were only two pediatric MGTs of the head and neck (cases 1 and 2). 15 Local invasion was reported in nine of 11 primary tumors and involved the trachea, larynx, esophagus, and carotid. Four patients developed distant metastases, most commonly in the lungs, brain, and skin (cases 1, 3, 9, and 10).…”

“…No consensus exists with regard to management of recurrent or metastatic disease. Only three reports exist of MGTs in children and adolescents, arising in the shoulder, arm, and neck . The rarity of these tumors in children makes establishing management plans difficult.…”

“…Only three reports exist of MGTs in children and adolescents, arising in the shoulder, 13 arm, 14 and neck. 15 The rarity of these tumors in children makes establishing management plans difficult. In this study, we review the relevant literature on MGTs of the head and neck and propose recommendations for evaluation and management.…”