Fibroid Arising From the Rudimentary Uterine Horn in MRKH Syndrome

Giant leiomyoma with extensive myxoid degeneration in Mayer–Rokitansky–Küster–Hauser syndrome

“…Myomas can form in the rudimentary uterine horns of patients with MRKH syndrome because Müllerian ducts have smooth muscles at their proximal ends, which can be affected by estrogen produced by the normal ovaries. Nevertheless, leiomyomas are rare in MRKH syndrome because of low concentration or sensitivity of estrogen receptors in the rudimentary horns …”

“…Nevertheless, leiomyomas are rare in MRKH syndrome because of low concentration or sensitivity of estrogen receptors in the rudimentary horns. 2 CT and magnetic resonance imaging are helpful in the diagnosis of leiomyoma in MRKH, the latter being 100% accurate. 3 On CT, leiomyomas appear as well-circumscribed masses isodense to hypodense compared with myometrium, with variable enhancement patterns, but leiomyoma with myxoid degeneration can appear as complex cystic masses.…”