Familial Schamberg’s Disease

Familial pigmented purpuric dermatoses

“…Consanguinity was not present in any of the cases described so far. These features are suggestive of an autosomal‐dominant inheritance pattern; similar observations have been made by previous authors 2,5 . Larger pedigrees need to be examined to confirm the pattern of inheritance.…”

“…Gould and Farber described a distinctive pigmented purpuric eruption closely resembling Schamberg's disease in six family members over three generations 2 . Kanwar and Thami described Schamberg's disease in four family members over two generations 5 . To the best of our knowledge, our case is the seventh report in the published work.…”

“…2 Kanwar and Thami described Schamberg's disease in four family members over two generations. 5 To the best of our knowledge, our case is the seventh report in the published work.…”

Lichen Aureus

“…29 The cause of PPPD and LA remains unknown. Familial cases 30 and associations with hematologic diseases, hepatic diseases, 31 and diabetes mellitus 32 have been reported. In some cases, LA has been related to allergic contact allergens such as paraphenylenediamine, cobalt, benzoyl peroxide, balsam of Peru, and glass wool.…”

Monoclonal Rearrangement of the T Cell Receptor Gamma-Chain in Lichenoid Pigmented Purpuric Dermatitis of Gougerot-Blum Responding to Topical Corticosteroid Therapy

“…Familial cases [11], the association with hematological and hepatic disease [7], diabetes mellitus [12]and drug ingestion (acetaminophen, carbomals, meprobamate, thiamine and chlordiazepoxide) [13]have been reported.…”