Erythromelanosis follicularis faciei et colli with reticulated hyperpigmentation of the extremities

Abstract

Key Clinical MessageErythromelanosis follicularis faciei et colli (EFFC) is a distinct, rare, and underdiagnosed condition of unknown etiology that is characterized by well‐demarcated erythema, hyperpigmentation, and follicular papules. The pigmentation is usually on both maxillary, preauricular regions, and the cheeks. We report a case of a 12‐year‐old boy with EFFC that was associated with reticulated pigmentation of the extremities.

Erythromelanosis follicularis faciei et colli: Dermoscopy and dermatopathology correlates

“…It affects equally males and females with a mean age of onset of 12 years. 3 It has been classified as subtype of keratosis pilaris. 4 In fact, our patient had no family history of EFFC and the matter begun at the age of 25 years.…”

“…Clinically, it is defined by the association of bilateral, symmetrical erythema, and brownish pigmentation, combined with follicular plugging. 3 However, cases of unilateral involvement have also been described. 5 Histopathology of EFFC typically shows follicular plugging, hyperkeratosis, and increased pigmentation in the basal layer.…”

Erythromelanosis Follicularis Faciei et Colli: A Case Report in a Caucasian Male and Brief Review of the Literature

“…Although EFFC is considered a rare disorder, it has been suggested that it actually may just be an underdiagnosed dermatosis [ 4 ]. The simultaneous presence of well-demarcated erythema, hyperpigmentation, and follicular papules in the facial and neck region should make one think of EFFC.…”