Erythromelanosis Follicularis Faciei: A Case Report and Review of the Literature

Abstract

Erythromelanosis follicularis faciei is a rare sporadic condition of unknown etiology characterized by reddish-brownish patches and follicular papules that appear commonly on the face and rarely on the neck. Herein, we report a 16-year-old male who had asymptomatic facial skin lesions since early childhood. His family history revealed a similar case in his younger brother. His parents are not consanguineous. Skin examination revealed diffuse nonscaly brownish patches with erythematous background and multiple skin-colored, hypopigmented follicular papules on both cheeks. A summary of previous reports of erythromelanosis follicularis faciei in the literature is presented in this report.

Co-existent erythromelanosis follicularis faciei et colli and erythroses pigmentosa mediofacialis in a patient of generalized keratosis pilaris - A rare report in a young female

“…[ 1 ] The male to female ratio is observed to be 2:1. [ 2 ] However, it is increasingly reported in female patients as noticed in our case. [ 3 ] EPM as described by Brocq, is erythematous to hyperpigmented, rough skin over midline of the face.…”

Keratosis pilaris rubra with mucin deposition

“…The KPA spectrum of KP is defined by the presence of atrophy, scarring, or alopecia and includes (a) KPA faciei/ulerythema ophryogenes, a scarring variant involving the lateral third of the eyebrows with skin atrophy; (b) atrophoderma vermiculatum, a variant with fibrosis and “honeycomb” atrophic lesions primarily of the cheeks; and (c) keratosis follicularis spinulosa decalvans, a variant with follicular plugging and scarring alopecia . EFFC involves a triad of erythema, hyperpigmentation, and folliculocentric papules on the face ( faciei ) and neck ( colli ) . KPR is characterized by confluent erythema as the predominant feature, with widespread involvement and persistence of disease after puberty .…”

Erythromelanosis follicularis faciei et colli with reticulated hyperpigmentation of the extremities

“…Poikiloderma of Civatte is seen in sides of the neck in middle‐aged women. Atrophoderma vermiculatum has honeycombed atrophy that affecting the cheeks, and no erythema or pigmentations are usually noticed .…”