Epidermólisis bullosa distrófica recesiva y embarazo

Boria, Félix; Maseda, R.; Martín-Cameán, María; Calle, María de la; Lucas, R. de

doi:10.1016/j.ad.2017.06.024

Cited by 6 publications

(2 citation statements)

References 11 publications

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“…A correlation between EB and intrauterine growth restriction has also been suggested [ 7 ]. Nevertheless, the evidence suggests that RDEB does not contraindicate pregnancy, although the risk of complications may be higher [ 8 ].…”

Section: Discussionmentioning

confidence: 99%

Squamous cell carcinoma in a pregnant woman with recessive dystrophic epidermolysis bullosa

Lopes¹,

Baptista

Moreira

2020

Oxford Medical Case Reports

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We report the case of a pregnant woman with recessive dystrophic epidermolysis bullosa. During pregnancy, she presents with a large, rapidly growing, tumor on her right forearm, whose biopsy revealed an invasive squamous cell carcinoma. Amputation by the middle third of the forearm was performed at 21 weeks of pregnancy, without intra- or post-operative complications. The remainder of pregnancy was unremarkable and, at 36 weeks, she gave birth to a healthy baby. One month after delivery, a large lymph node conglomerate was detected in the right axilla, highly suggestive of metastatic disease and complete lymph node dissection was then performed. Despite the prompt institution of chemotherapy, the patient died a few months later due to metastatic disease.

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Section: Discussionmentioning

confidence: 99%

Squamous cell carcinoma in a pregnant woman with recessive dystrophic epidermolysis bullosa

Lopes¹,

Baptista

Moreira

2020

Oxford Medical Case Reports

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“…Pregnancy is relatively uncommon, due to the associated disability and concerns regarding affected children [8,9]. Nevertheless, successful pregnancy outcomes have been reported even in women with severe types of EB [3,[9], [10], [11], [12], [13]]. Women with EB are not at increased risk of pregnancy-related complications [8], and the skin itself does not seem to worsen during pregnancy [9].…”

Section: Discussionmentioning

confidence: 99%

Management of epidermolysis bullosa simplex in pregnancy: A case report

Shah

Kumaraswami

Mushi

2019

Case Reports in Women's Health

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Epidermolysis bullosa (EB) encompasses a group of diseases characterized by extreme fragility of skin and mucous membranes, resulting in blister formation following minimal injury. There are 4 types of EB, with epidermolysis bullosa simplex (EBS) being the most common. We report our experience with the care of a parturient woman diagnosed with EBS. There is little literature on pregnancy in women with this condition. Special precautions are necessary during diagnostic and therapeutic interventions to avoid bullae formation or exacerbation of existing lesions. Frictional or shearing forces are typically more damaging than compressive forces. Multidisciplinary planning was done for our patient to ensure uneventful labor and delivery. Elective induction of labor was started at 40 weeks of gestation. She eventually underwent a cesarean delivery after failed trial of labor. We present this case to highlight the obstetric and anesthetic implications of caring for a parturient with EBS.

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