Arachnoid cysts are collections of cerebrospinal fluid surrounded by an arachnoid membrane. Most of them are asymptomatic and are detected incidentally on imaging studies. Others reveal themselves with a variety of clinical symptoms depending on their size and location. Although most located in the temporal fossa, cysts can be found in any compartment of the brain or spinal cord. Posterior fossa arachnoid cysts (PFAC) account for 5-48% of all arachnoid cysts. In this case series, we analyze relevant features of 27 PFAC reviewed in an ataxia and other rare diseases clinic.